Mobius syndrome: a dental hygiene case study and review of the literature

Abstract

Mobius syndrome, a rare, non-progressive, congenital neuromuscular disorder, presents with multiple dental and medical complications. Signs and symptoms of this condition include: congenital, bilateral or unilateral palsies of the facial and abducens cranial nerves (cardinal sign), and a broad scope of multisystem abnormalities, which may or may not include the following: opthalmoplegia externa, lingual palsy, clubfoot, branchial malformation, ptosis, mental retardation, and pectoralis muscle defect. From a dental standpoint, a number of anomalies may manifest, including: multiple congenitally missing teeth (both deciduous and permanent), micrognathia, paralysis and hypoplasia of the tongue, absence of facial expression and weakness of the palate. This article reviews the case study of a 40-year-old male client with Mobius syndrome, dental hygiene diagnosis (DHDx) and intervention, and the dental hygienists' responsibility and role in care.

Management of maxillofacial hard and soft tissue discrepancy in Möbius sequence: Clinical report and review of the literature

“…Facial palsy management with microneurovascular free-muscle transfer has been widely addressed in the scientific literature (Johnson et al, 1997;Ueda et al, 1998;Zuker et al, 2000;Goldberg et al, 2003;Bae et al, 2006;Bianchi et al, 2009). The issues of increased risk of periodontal disease and dental caries have been considered previously too (Serpa-Pinto et al, 2002;Sensat, 2003;Magalhaes et al, 2006;Scarpelli et al, 2008;Lima et al, 2009). However, to our knowledge, the problem of malocclusion has only been mentioned once in the scientific literature (Chou et al, 2010).…”

“…Although it is considered a rare condition by various authors (Strömland et al, 2002;Verzijl et al, 2003;Sensat, 2003), the global incidence and prevalence remain undetermined. Males and females seem to be affected equally (Gorlin et al, 1990).…”

“…Most patients do not have strabismus when looking straight-ahead, but they tend to turn their head to compensate for the limitation of movement horizontally (Strömland et al, 2002). Ptosis, nystagmus, conjunctivitis and abnormal lacrimation may be present too (Karoluk and Lanigan, 1989;Strömland et al, 2002;Sensat, 2003).…”

Estudo da mastigação e da deglutição em crianças e adolescentes com Sequência de Möbius

“…Nos dentes, pode haver hipoplasia dentária e oclusão tipo Classe II de Angle. Geralmente, o palato duro é profundo, podendo, em alguns casos, ocorrer fissura palatina (17)(18)(19) . No Sistema Nervoso Central, pode haver alterações neurológicas, mas em 90% dos casos a inteligência está preservada (20) .…”

Oral findings and dental management of a patient with Moebius syndrome: a case report

“…T, thorax). Each of the above areas is rated on a scale of zero to three, and a higher grade means a more severe anomaly 7) . Although several patients have reportedly had diminished intelligence, mental retardation is reported just 10% of cases 10) .…”