Meeting the complex care needs of a patient with Darier's disease

Abstract

An interdisciplinary team reduced the cost and duration of hospital care for a patient with this debilitating skin disease, with the help of an air-fluidised bed. Nursing time was reduced, yet the patient's quality of life improved dramatically.

Darier's (Darier–White) disease/keratosis follicularis

“…Mild cases require emollient, sunscreen, and protection from very hot environments only. In moderate and severe cases, several modalities have been attempted with variable success 1,4,25,132–136 . Of the oral retinoids, both acetretin and isotretinoin have been proven to be quite promising 137–141 .…”

“…In moderate and severe cases, several modalities have been attempted with variable success. 1,4,25,[132][133][134][135][136] Of the oral retinoids, both acetretin and isotretinoin have been proven to be quite promising. [137][138][139][140][141] Topical tretinoin (alltrans -retinoic acid) and Bcis -retinoic acid have shown a differential response; [141][142][143] however, irritation limits their value.…”