Medulloepithelioma of the Optic Nerve Head

Cerebral Medulloepithelioma With Long Survival -Case Report-

“…[1][2][3][4][5][6][7][8][9][10][11][12][13][14][15][16][17][18][19][21][22][23][24][25][26][27][28][29][30][31][32][33][34][35][36][37][38][39][40][42][43][44][45] Although most medulloepitheliomas manifest in the first decade of life, 1,11,13,15,22,25,28,31,39,40,…”

“…1,6,10,11,21,22,28,31,38,40,44) On the other hand, intraorbital, 7,8,15,30) peripheral, 26) and cauda equina 22) medulloepitheliomas have a much less malignant course and even those treated primarily or only by enucleation tend not to recur for a long time. 7,15,19,27) Extracranial and intracranial medulloepitheliomas have similar histological features, 8,30) and the great difference in the prognosis remains to be elucidated. In addition, the differences in the biological characteristics and behaviors of these neoplasms are unexplained.…”

Malignant non-teratoid medulloepithelioma with submandibular metastases

“…The tumor typically occurs in children aged between 2 and 4 years, but its diagnosis is often delayed despite the onset of symptoms because of the rarity of the tumor [2]. These tumors are characteristically unilateral and sporadic [3].…”

Colossal Malignant Nonteratoid Medulloepithelioma of the Eye with Unusual Metastases: The Natural History

“…[1][2][3] The use of local irradiation (scleral plaque or proton beam) or chemotherapy has not been established; it is only recommended for local recurrence or distant metastases. 4,5 The treatment strategy and clinical outcomes of extensive medulloepithelioma with metastases have not been previously assessed. In view of the large size and extensive metastases chemotherapy was initially administered which however did not produce any appreciable change in the tumor.…”