Massive renal angiomyolipoma in tuberous sclerosis

Katz, Douglas S.; Poster, Robert B.

doi:10.1016/s0899-7071(96)00019-8

Cited by 15 publications

(16 citation statements)

References 10 publications

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“…This giant lesion surpasses the AML mass weighing 6300 g in a case associated with TS reported by Rosselló Barbará et al,[6] and the lesion (weighing 3500 g each) in the cases reported by Tsutsumi et al,[5] and Katz and Poster. [7] The only other AML, which has dimensions larger than the present one (39 cm × 25 cm × 9 cm) has been reported by Katz and Poster, where the mass measured 45 cm × 20 cm × 15 cm and weighed 3500 g (weight less than 7500 g measured in the present case), and was associated with TS. [7] Thus the present case is the largest sporadic renal AML in size and heaviest renal AML in both syndromic and sporadic categories ever reported in the literature.…”

Section: Discussionmentioning

confidence: 54%

“…[7] The only other AML, which has dimensions larger than the present one (39 cm × 25 cm × 9 cm) has been reported by Katz and Poster, where the mass measured 45 cm × 20 cm × 15 cm and weighed 3500 g (weight less than 7500 g measured in the present case), and was associated with TS. [7] Thus the present case is the largest sporadic renal AML in size and heaviest renal AML in both syndromic and sporadic categories ever reported in the literature.…”

Section: Discussionmentioning

confidence: 56%

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Giant Renal Angiomyolipoma: Unusual Cause of Huge Abdominal Mass

Taneja

Singh²

2013

Journal of Clinical Imaging Science

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We present the imaging and histopathological characteristics of a giant renal angiomyolipoma (AML) in a 49-year-old female patient, who presented with bloating sensation in the abdomen and a steadily increasing abdominal girth for about 3 years. Contrast enhanced computed tomography (CECT) scan films of abdomen revealed that a large fat containing tumor had replaced the left kidney while displacing the rest of the abdominal contents toward the other side of the midline. Intraoperatively the left kidney was completely replaced by a fat containing tumor. The recovered surgical specimen measured 39 cm × 25 cm × 9 cm and weighed 7500 g. Histopathological investigation with immuno-histochemical staining of the specimen with hydroxy beta-methylbutyric acid-45 confirmed this lesion as AML. CECT scan of the head did not show any lesion suggestive of tuberous sclerosis. The giant tumor of the present case is the heaviest AML in both syndromic and sporadic categories and largest by dimensions as sporadic AML ever reported in the literature.

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Section: Discussionmentioning

confidence: 54%

Section: Discussionmentioning

confidence: 56%

Giant Renal Angiomyolipoma: Unusual Cause of Huge Abdominal Mass

Taneja

Singh²

2013

Journal of Clinical Imaging Science

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“…2 However, cases of massive AMLs (measuring up to 45 × 20 × 15 cm) have also been reported. 3 Sporadic AMLs have a female preponderance, occurring between the ages of 30 and 50 years, and are more often unilateral and larger in size. 1 …”

Section: Discussionmentioning

confidence: 99%

Managing a massive renal angiomyolipoma

et al. 2012

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“…Bilateral olan olgularda nefrektomiden kaçınılsa da, özel-likle hemoraji kontrolü amacıyla nefrektomi gerekebilir. Alternatif yaklaşımlar elektif arteriyel embolizasyon ve parsiyel nefrektomidir (1,2). Sonuç olarak; tüberosklerozda nadiren geniş boyutlarda renal AML'ler görülür.…”

Section: Discussionunclassified

“…TS'li olguların %40-80'inde böbreklerde küçük, sıklıkla asemptomatik, bilateral ve multipl anjiyomyolipom (AML)'lar görülmektedir. Yirmi santimetreden büyük AML'ler oldukça nadirdir (1,2). Bu yazı ile, her iki böbreğinde dev anjiyomyolipomları olan olgunun bilgisayarlı tomografi (BT) bulguları sunularak, konuyla ilgili kaynaklar gözden geçirildi.…”

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Tüberosklerozda dev renal anjiyomyolipomlar: Bilgisayarlı tomografi bulguları Giant Renal Angiomyolipomas in Tuberous Sclerosis: Computed Tomography Findings

Nisa¹

2005

Ankara Üniversitesi Tıp Fakültesi Mecmuası

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Tüberoskleroz, tüm organları tutabilen ancak en sık deri, beyin, kalp, göz ve böbreği tutan benign hamartomatöz lezyonlar ile karakterize otozomal dominant bir hastalıktır. Tüberosklerozluların %40-80'inde bilateral, multipl, küçük ve sıklıkla asemptomatik renal anjiyomyolipomlar görül-mektedir. Ancak sunulan olguda olduğu gibi boyutları 20 cm'yi aşan anjiyomyolipomlar oldukça nadirdir. Boyutları büyüdükçe semptomatik olma olasılığı ve masif, hatta fatal hemorajiyle sonuçlanan spontan rüptür riski artmaktadır. Bilgisayarlı tomografi, düşük oranlardaki yağ içeriğini bile saptayabilmesi nedeniyle, renal anjiyomyolipomların tanısında ilk tercih edilen görüntüleme yöntemidir. Anahtar sözcükler: anjiyomyolipom, bilgisayarlı tomografi, tuberosklerozTuberous sclerosis is an autosomal dominant disorder characterized by hamartomas that may occur in any organ system, but most often occur in skin, brain, heart, eye and kidney. Between 40 and 80% of patients with tuberous sclerosis have renal angiomyolipomas which are often bilateral, multifocal, small and often asymptomatic. Very large renal angiomyolipoma, like the case reported here, are very rare. They are often symptomatic and have a propensity for spontaneous rupture, resulting in massive and at times, fatal hemorrhage. Because of its sensitivity in detecting small amounts of fat, computed tomography is imaging modality of choice in the diagnosis of renal angiomyolipomas.

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Massive renal angiomyolipoma in tuberous sclerosis

Cited by 15 publications

References 10 publications

Giant Renal Angiomyolipoma: Unusual Cause of Huge Abdominal Mass

Giant Renal Angiomyolipoma: Unusual Cause of Huge Abdominal Mass

Managing a massive renal angiomyolipoma

Tüberosklerozda dev renal anjiyomyolipomlar: Bilgisayarlı tomografi bulguları Giant Renal Angiomyolipomas in Tuberous Sclerosis: Computed Tomography Findings

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