Massive fibrous dysplasia of the temporal bone

Exostosis of the internal auditory canal

“…The absence of generalized bone involvement or increased serum alkaline phosphatase can eliminate Paget's disease from the diagnosis (Applebaum and Clemis, 1977;Edelken, 1981;Griffey, 1960;Nager, 1975;Proope etal., 1985). Fibrous dysplasia is characterized by spiculation, diffuse involvement of the entire temporal bone by the fibro-osseous process and/or raised intracranial tension, and involvement of other bones, (Chatterji, 1974;Edeiken, 1981;Nager etal., 1982;Zizmor and Nojek, 1969). Congenital aplasia of the inner ear structures may produce small canals due to failure of the supplying nerve development; they are usually associated with ossicular abnormalities or agenesis of the external ear (Pagani et al, 1980;Phelps etal., 1975;Portmann et al, 1975).…”

Medical management of sensorineural hearing loss PART II: Musculo-skeletal system

“…Two cases have shown sensorineural hearing loss, one due to encroachment on the internal auditory canal, and the other due to a labyrinthine fistula (Chatterji, 1974;Cohen and Rosenwasser, 1969, respectively).…”