Management of Uterine Didelphys With Unilateral Cervico-Vaginal Agenesis Mimicking Ohvira

Abstract

Background: Sarcoma botryoides is a variant of embryonal rhabdomyosarcoma. This malignant tumor originates from muscle progenitor cells and although it is highly malignant, cure rates exceed 90%. 1 While rhabdomyosarcoma is the most common soft tissue malignancy in children, vaginal presentation is rare. 2 The average age of diagnosis of vaginal rhabdomyosarcoma is 21 months of age. Treatment consists of chemotherapy combined with local radiation to achieve local tumor control while preserving organ function. 1 Sequelae of vaginal radiation therapy in this age group have not been well defined. However, vaginal stenosis is a known result of local radiation therapy in adult women treated for a variety of pelvic cancers. In adults, vaginal dilation is the primary method of prevention and treatment. 3 Case: An 18-month-old child presented with vaginal bleeding and was