Anomalies of the aortic arch complex (vascular rings) occur in various forms, often causing tracheal and esophageal compression. [1][2][3][4][5] We describe a rare case of recurrent strokes resulting from thrombus in remnant of a repaired right aortic arch stump.
CLINICAL SUMMARYA 50-year-old man with spina bifida was seen with a history of recurrent strokes during the previous 3 years. He had undergone ligation of patent ductus arteriosus and ''aortopexy'' through left thoracotomy 40 years previously. Seven years previously, he had had dysphagia caused by esophageal compression, which was attributed to vascular ring equivalent resulting from right-sided ''cervical'' aortic arch with an aberrant left subclavian artery coming off a remnant of aneurysmal mid-descending aorta. The right arch coursed leftward at the level of the carina, crossing the spine and compressing the esophagus before descending on the left side of spine with aneurysmal dilatation of the mid-descending aorta.The esophagus was compressed by the confluence of the dilated distal right aortic arch/proximal descending thoracic aorta, the carina, and the azygos vein. At that time, the patient From the Department of Thoracic and Cardiovascular Surgery, Heart and Vascular Institute, Cleveland Clinic, Cleveland, Ohio. Disclosures: Authors have nothing to disclose with regard to commercial support.