Management of Craniofacial Development in the Parry-Romberg Syndrome: Report of Two Patients

Abstract

The use of orthodontic therapy allows patients affected by hemifacial progressive atrophy to present a more harmonic face at the end of puberty when final reconstruction can be planned. These results provide for a limitation of surgical intervention to the sclerodermic area alone.

A review of Parry-Romberg syndrome

“…143 Orthodontic rehabilitation 144 and the use of prophylactic orthodontic appliances were described with good results. 145 …”

Odontostomatologic involvement in juvenile localised scleroderma of the face

“…This is the first study which systematically investigated the odontostomatologic involvement of LSF with a multidisciplinary protocol. Previously, isolated odontostomatologic abnormalities have been reported only in small series or single case reports 3,10–17 . All patients in our series showed at least one odontostomatologic alteration such as root underdevelopment, resorption and dilacerations, detected in 27.3%.…”

“…Similar abnormalities, described in the literature, were attributed to the spatial and temporal coincidence between permanent teeth formation and active stage of disease. Root defects can lead to missing teeth and even dental malocclusion 11–17 …”

“…The OPG was used to identify possible root abnormalities (resorption, dilacerations, underdevelopment). Skeletal symmetry was evaluated by OPG through the Habets index, which measures the height of the mandibular ramus and the condyle of the affected side compared to the contralateral 15 . Cephalometric analysis, performed on lateral view according to the Ricketts–Roth–Jarabak and Roth–Jarabak methods through the software Dolphin, provided a complete evaluation of the skeletal occlusal class and facial growth.…”

“…Despite its quite frequent clinical observation, the odontostomatologic involvement of LSF has not been systematically described in the literature, although few case reports exist 3,10–17 …”