Introduction: Twin ectopic pregnancy is a rare event that affects 1:125,000 pregnancies. There are around 100 reported cases in the literature, 15 cases with the presence of fetal heartbeat diagnosed by ultrasound examination. It is important to highlight that early diagnosis is essential to avoid serious complications, including maternal death. Case Report: 36 years old anovulatory patient underwent intrauterine insemination, with a positive result, having been subsequently diagnosed with early unilateral ectopic twin pregnancy at 6 weeks. The patient underwent video laparoscopic left salpingectomy and was discharged the following day. Discussion: Early diagnosis is essential so that treatment can be instituted as quickly as possible, as this is an event with high morbidity and mortality.