Malignant Rhabdoid Tumor of the Adrenal Gland: Case Report and Review of the Literature

Abstract

Malignant rhabdoid tumor was first thought to be a subtype of wilm’s tumor, which was later disproven by Haas et al. and was categorized as a separate entity. Malignant rhabdoid tumors are mainly present in the kidneys of children, however, cases of extra renal malignant rhabdoid tumor were reported in the literature. In this report we describe a case of extra renal malignant rhabdoid tumor in the adrenal gland. Malignant rhabdoid tumor is a highly aggressive neoplasm with very poor prognosis. Due to the rarity of the disease, no universal treatment regimen has been developed yet, where treatment options include the surgical removal of the tumor, chemotherapy, radiotherapy, or a multimodality approach of management. In this report we present a case of 21-year-old lady with MRT in the adrenal gland, who had neoadjuvant radio-chemotherapy followed by laparoscopic adrenalectomy.

Primary Adrenal Malignant Rhabdoid Tumor in a 14-Year-Old Female: A Case Report and Literature Review

“…There were only 3 cases of primary MRT and 4 cases of primary ES in the adrenal gland reported in the English literature (Table 1). [8][9][10][11][12][13][14] Only 1 of the 3 MRT cases occurred in a patient younger than 5 years. All 4 ES cases occurred in patients older than 10 years.…”