Malignant Peripheral Nerve Sheath Tumor of the Infratemporal Fossa

Abstract

Malignant peripheral nerve sheath tumor is a rare pathologic lesion in a patient without neurofibromatosis diseases. The patient is a 36-year-old man without any congenital or systemic diseases who presented with a firm and painful mass on the left preauricular and temporomandibular joint area with paresthesia of temporal region. Clinical diagnosis of this tumor was made with delay owing to the lack of initial sign and symptoms and its location.

Excision of recurrent synovial sarcoma of the infratemporal fossa

“…The types of tumors make up a long list, including adenoid cystic tumor, meningioma, benign and malignant peripheral nerve tumors, lipoma, hemangiopericytoma, giant cell tumor, relapsing benign parotid tumors, histofibroma, rhabdomyosarcoma, fibrosarcoma and SS. [4][5][6][7][8] Infratemporal fossa metastatic lesions noted in the literature are malignant meningioma, adrenal tumor and papillary thyroid cancer. [1] Synovial sarcoma is a rare cancer type, which is primarily derived from the soft tissues of the lower extremities.…”

“…Total excision of ITF located SS is challenging because of vital structures, and additive treatments are required. [4][5][6] Along with understanding the anatomy, various surgical approaches developed for ITF masses recommend total excision with maximal exposure and minimal morbidity. If needed, these approaches can be combined.…”

Computed tomography and magnetic resonance imaging of lesions at masticator space

“…It may be difficult to distinguish malignant from benign growths. Large tumor size (C5 cm), ill-defined infiltrative margins, rapid growth, tumor signal intensity, heterogeneity, and erosion of the skull base foramina out of proportion to tumor size suggest an underlying malignant nature [29] (Fig. 8).…”