Maladie d’Erdheim-Chester cérébrale avec double lésion pseudotumorale et ischémique

Amézyane, T.; Abouzahir, A.; Bassou, D.; Zoubeir, Y.; Hammi, S.; Mahassin, F.; Ohayon, V.; Archane, M. I.

doi:10.1016/j.neurol.2008.10.006

Cited by 5 publications

(1 citation statement)

References 19 publications

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“…However, three of these 5 observations are questionable. In the case of Amezyane et al [ 11 ] a focal stroke was discovered on brain MRI, but was probably asymptomatic and did not explain the neurological deficit (due to a brain pseudonodular lesion of ECD); in the case of Mergancova et al, [ 14 ] there were incomplete criteria of ECD; finally, Mélé et al [ 21 ] described a patient with mixed histiocytosis (with both Langerhans and non-Langerhans forms in the same patient). Interestingly, in the other cases (as in the case of Mergancova et al [ 14 ] ), vascular involvement (periarterial infiltration and sometimes stenosis) was observed in the supra-aortic arteries, whereas patients had no cardiovascular risk factors.…”

Section: Discussionmentioning

confidence: 99%

Long-term outcome of basilar stenosis in Erdheim–Chester disease

et al. 2016

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Background:Erdheim–Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis. This inflammatory myeloid neoplasm is frequently complicated by neurological symptoms, but stroke is an exceptional manifestation of this disease.Methods:We report the case of a 59-year-old woman who presented a vertebrobasilar stroke secondary to infiltration and severe stenosis of the basilar artery, improved after interferon-alpha therapy. We performed a review of the relevant literature and reported the few other cases described.Results:With our patient, we have found only 7 observations of cerebrovascular disorder in ECD. Most of them had supravascular arteries involvement.Conclusion:Stroke is a rare treatable and potentially reversible complication of ECD. The pathophysiological processes explaining stroke in this disease are uncertain, but periarterial stenosis of cerebral arteries may be a mechanism.

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Section: Discussionmentioning

confidence: 99%

Long-term outcome of basilar stenosis in Erdheim–Chester disease

et al. 2016

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Xanthogranulomatous osteomyelitis

Borjian

Rezaei

Eshaghi

et al. 2011

J Orthopaed Traumatol

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Xanthogranulomatous osteomyelitis is a rare type of inflammatory process which is characterized by composition of immune cell aggregation on histological studies. Delayed-type hypersensitivity reaction of cell-mediated immunity may be implicated in its pathogenesis. Gross and radiological examination can mimic malignancy, and differentiation should be confirmed by histopathological evaluation. We describe the case of a 14-year-old Afghan boy presenting with pain in right shoulder and left leg with prior history of trauma. Fever, limitation in right shoulder range of motion, and tenderness in right shoulder and left thigh were detected following examination. Mild leukocytosis, elevated alkaline phosphatase, and increased erythrocyte sedimentation rate with negative C-reactive protein (CRP) were revealed. X-ray imaging showed mixed density, periosteal reaction, and cortical disruption. Computed tomography (CT) scan revealed lesions involving medulla and cortex, periosteal reaction with soft tissue component, and bone marrow infiltration in right humerus and left fibula. On magnetic resonance imaging (MRI), signal abnormalities in medulla, metaphysis, and diaphysis of the left fibula associated with cortical irregularity and diffuse soft tissue hypersignal areas were demonstrated. Finally, xanthogranulomatous osteomyelitis was confirmed by histological sample. The clinical manifestations and radiographic and laboratory findings of this rare condition are discussed.

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