Lymphangioma circumscriptum of the vulva and Klippel-Trenaunay syndrome

Abstract

Lymphangioma circumscriptum is a rare vascular malformation affecting the lymphatic vessels of the papillary dermis [1]. Klippel-Trenaunay sydrome is a congenital vascular malformation characterized by venous varicosities, soft tissue and/or bony hypertrophy [2]. Here we report a case of association of Lymphangioma circumscriptum of the vulva and Klippel-Trenaunay syndrome.