Lung Transplantation Outcomes for Pulmonary Alveolar Microlithiasis: A Limited Case Series.

Moon, Eunice; Tsuang, Wayne; Bonnette, P.; Jackson, Katherine; Lien, Dale; Blumenthal, Nancy P.; Kotloff, Robert M.; Ahya, Vivek N.

doi:10.1164/ajrccm-conference.2009.179.1_meetingabstracts.a4602

Cited by 7 publications

(15 citation statements)

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“…transplantations instead of unilateral transplants on the grounds of resistant shunt development in a lung transplantation series of 14 cases, one of which was caused by PAM 12 . Besides, no recurrence was detected in the presented cases or series 7,8,10,13,14 . Moon et al reported the case of a patient who survived for 15 postoperative years with no recurrence after the lung transplantation was performed after PAM diagnosis 8 .…”

Section: Discussionmentioning

confidence: 51%

“…Besides, no recurrence was detected in the presented cases or series 7,8,10,13,14 . Moon et al reported the case of a patient who survived for 15 postoperative years with no recurrence after the lung transplantation was performed after PAM diagnosis 8 . In their series, Shigemura et al reported no recurrence and only two cases of postoperative major bleeding after bilateral lung transplantation 15 .…”

Section: Discussionmentioning

confidence: 51%

“…Lung transplantation is a treatment option for PAM patients and is recommended in severe cases of oxygen dependent respiratory failure before the onset of right heart failure 7,8,10 . Bonette et al recommended bilateral lung -The risk of recurrence should not be considered as a justifying reason to avoid the transplantation option.…”

Section: Discussionmentioning

confidence: 99%

“…The only known treatment is lung transplantation performed before the onset of right heart failure. No recurrence has been reported after transplantation 7,8 . Here we present the case report of the first Turkish patient followed-up in the intensive care unit (ICU) with the diagnosis of PAM, who needed ventilator support at the time of discharge from the ICU and received lung transplantation in Austria.…”

Section: Introductionmentioning

confidence: 95%

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Lung transplantation in an intensive care patient with pulmonary alveolar microlithiasis - a case report

Güçyetmez¹,

Ogan²,

Ayyıldız³

et al. 2014

F1000Res

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Section: Discussionmentioning

confidence: 51%

Section: Discussionmentioning

confidence: 51%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 95%

See 2 more Smart Citations

Lung transplantation in an intensive care patient with pulmonary alveolar microlithiasis - a case report

Güçyetmez¹,

Ogan²,

Ayyıldız³

et al. 2014

F1000Res

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“…El diagnóstico definitivo es histopatológico a través de una biopsia de pulmón a cielo abierto o transbronquial 14,15,18 . En el presente caso se indicó la biopsia a cielo abierto, a fin de hacer una exploración exhaustiva y tomar un espécimen apropiado para el examen microscópico de la pieza.…”

Section: Discussionunclassified

Microlitiasis alveolar pulmonar: presentación de un caso

et al. 2018

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La microlitiasis alveolar pulmonar es una enfermedad rara cuya principal característica es la acumulación de sales de calcio dentro del alvéolo pulmonar, esto debido a la presencia de una mutación genética autosómica recesiva. Esta entidad se encuentra dentro del grupo de enfermedades pulmonares difusas y el diagnóstico principal es un reto para los profesionales de la salud. No existe un tratamiento hasta la fecha; se ha planteado el uso de bisfosfonatos, los esteroides y lavado bronco alveolar sin llegar a resultados concluyentes. Se prefiere llevar a cabo el trasplante pulmonar, para mejores resultados, antes de que se haya establecido el desarrollo de la insuficiencia ventricular derecha. El diagnóstico definitivo es histopatológico. De acuerdo con la literatura nacional publicada, a nuestro alcance, en Perú se ha reportado esta enfermedad tan solo con sospecha radiológica, sin publicar el diagnóstico histopatológico definitivo. Presentamos un caso diagnosticado en el Departamento de Cirugía de Tórax y Cardiovascular del Hospital Nacional Hipólito Unanue de Lima.

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Pulmonary alveolar microlithiasis. State-of-the-art review

Francisco

Silva

Hochhegger

et al. 2013

Respiratory Medicine

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Pulmonary alveolar microlithiasis (PAM) is a rare genetic lung disease characterized by calcifications within the alveoli. Mutations in the SLC34A2 gene, which encodes a type IIb sodium-phosphate cotransporter, are responsible for this disease, leading to intra-alveolar accumulation of phosphate that favors the formation of microliths. The hallmark of this disorder is clinical-radiological dissociation, with typical imaging findings that correlate well with specific pathological findings. The long-term prognosis is poor and no treatment has been discovered to date. The aim of this review is to describe the main pathological, clinical, and imaging aspects of PAM, ranging from its genetic basis to treatment.

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Lung Transplantation Outcomes for Pulmonary Alveolar Microlithiasis: A Limited Case Series.

Cited by 7 publications

References 0 publications

Lung transplantation in an intensive care patient with pulmonary alveolar microlithiasis - a case report

Lung transplantation in an intensive care patient with pulmonary alveolar microlithiasis - a case report

Microlitiasis alveolar pulmonar: presentación de un caso

Pulmonary alveolar microlithiasis. State-of-the-art review

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