Lumbocostovertebral syndrome with associated VACTERL anomaly

Lyngdoh, Toijam Soni; Mahalik, Santosh Kumar; Naredi, Bikash Kumar; Samujh, Ram; Khanna, Sudhansoo

doi:10.1016/j.jpedsurg.2010.06.005

Cited by 7 publications

(3 citation statements)

References 7 publications

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“…1 An abdominal hernia was recently safely treated using laparoscopic surgery, and lumbar hernia can theoretically be treated using a similar method. 6,8 In our case, the association between meningocele and the adjacent organs needed to be carefully determined before and during surgery. Once the meningocele was detached and repaired, the lumbar hernia was treated successfully under laparoscopic surgery through the typical procedure.…”

Section: Discussionmentioning

confidence: 99%

Thoracic meningocele in lumbo-costo-vertebral syndrome in a child: possible enlargement with repeated motion by anchoring to the diaphragm

Wataya¹,

Horikawa²,

Kitagawa³

et al. 2016

PED

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Lumbo-costo-vertebral syndrome (LCVS) is a rare disorder in children that is characterized by hemivertebrae, congenital absence of ribs, meningocele, and hypoplasia of the truncal and abdominal wall presenting as a congenital lumbar hernia. An otherwise healthy 12-month-old girl was referred to the authors' hospital with soft swelling on her left middle back; scoliosis had been present since birth. Imaging revealed a thoracic meningocele, ectopia of the spleen suggesting lumbar hernia, multiple anomalies of the thoracic vertebral columns, and defects of the ribs; thus, LCVS was diagnosed. Surgical observation revealed that the meningocele was firmly anchored to part of the diaphragm, which created stretching tension in the meningocele continuously with exhalation. Once detached, the meningocele shrank spontaneously and never developed again after cauterization. In this case, continuous or pulsatile pressure in the presence of a vertebral defect was thus considered to be an important factor for formation of the thoracic meningocele.

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Section: Discussionmentioning

confidence: 99%

Thoracic meningocele in lumbo-costo-vertebral syndrome in a child: possible enlargement with repeated motion by anchoring to the diaphragm

Wataya¹,

Horikawa²,

Kitagawa³

et al. 2016

PED

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“…All rights reserved. Harris et al, 2009;Helderman-van den Enden et al, 1997;Jones et al, 2010;Kapoor et al, 2014;Krishnamurthy and Kapoor, 2009;Lafer, 1994;Lazier et al, 2016;Lyngdoh et al, 2010;Montes-Tapia et al, 2016;Rattan et al, 2016;Sengar et al, 2011;Sharma et al, 2012;Singh et al, 2010;Somuncu et al, 1997;Vagholkar and Dastoor, 2013;Wataya et al, 2016).…”

Section: Literature Reviewmentioning

confidence: 99%

Congenital lumbar hernia–A feature of diabetic embryopathy?

Stevens

Hogue

Hopkin

et al. 2018

American J of Med Genetics Pt A

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“…[2] VACTERL anomaly has been reported in combination with LCVS. [3] LCVS with syringomyelia, posterior spinal dysraphism, and lipomas adherent through a spina bifida to the dorsal surface of a tethered spinal cord was treated with lumbar exploration and laminectomy in one report. [4] There are no treatment guidelines are available as handful of cases are reported.…”

Section: Dear Sirmentioning

confidence: 99%