Long-term outcome of asymptomatic patients with congenital cystic adenomatoid malformation

Abstract

This study suggests patients who present with asymptomatic CCAM will subsequently become symptomatic. Early surgical referral and intervention may be beneficial to avoid the development of complications.

Congenital cystic adenomatoid malformation of lung type 1

“…Congenital cystic adenomatoid malformations are classified into 5 types-0 to 4-using the Stocker classification [3][4][5]. Type 1 is associated with the best overall prognosis and may remain undetected until later in life, as in the present case.…”

Thoracoscopic segmentectomy for treatment of congenital lung malformations

“…Lobectomy is considered by some to be the procedure of choice for removal of CLMs [12][13][14][15] because complete resection of the diseased lobe leaves no possibility for residual disease [16,17] and the resultant risk of recurrent infection or malignant transformation [18][19][20][21][22]. In addition, some authors have speculated that the rate of postoperative air leak is less with lobectomy [3].…”

Congenital Pulmonary Malformation in Children

“…Sauvat et al, reported that 3 out of 29 patients with CPAM experience symptoms during the first weeks of life [17]. As many as 86% (18 out of 21) of patients, who were asymptomatic at birth, had become symptomatic by 13 years of age (median age of 2 years) [22]. In patients with CPAM, pneumonia with or without infected CPAM was reported in 43%, respiratory distress in 14%, and spontaneous pneumothorax in 14% [22].…”