Lipoid proteinosis

Lipoid proteinosis: Review of Indian cases

“…[ 3 8 ] Twelve cases have been found with such radiographic changes. [ 5 6 8 17 18 20 33 ] In the present case also along with typical radiographic changes, the absence of all 2 nd premolars was found giving typical case of LP.…”

“…Hence, review of 51 cases of LP reported in India from 1969 to 2021 is done along with the present case [ Table 1a – c ]. [ 1 4 5 6 8 9 10 11 12 13 14 15 16 17 18 19 20 21 22 23 24 25 26 27 28 29 30 31 32 33 34 35 36 37 38 39 40 41 42 43 44 ] LP is more reported in patients in the age group of 11-20 (51%). More prevalence of LP is reported in males (70.6%).…”

“…On review of oral manifestations, 42 cases were found as shown in Table 1c . [ 1 4 5 8 9 10 11 12 13 14 15 16 17 18 19 20 21 22 23 25 26 27 28 29 30 31 32 33 34 35 37 38 39 42 43 44 ] The most common involved site is tongue with typical thick woody appearance followed by restricted tongue movements. In the present case, also similar findings were present.…”

“…Only 10 cases have reported systemic involvement in which, the most common feature is seizure and mental retardation. [ 5 9 14 15 16 17 18 19 20 ]…”

Lipoid proteinosis: Curious case of two siblings!

“…Treatment modalities reported in the literature include oral steroids, dimethyl sulphoxide, intralesional heparin, and etretinat. [ 6 ]…”