“…1 To the best of our knowledge, less than 100 cases of patients with AO linear scleroderma ECDS have been reported. 2,4,[5][6][7][8][9][10][11][12][13][14][15][16][17] Patient descriptions of AO localized scleroderma are summarized in Table 1. Of note, while AO ECDS is very rare, ECDS localized scleroderma developing in a patient with pre-existing localized scleroderma is exceedingly rare.…”