Linear Morphea- A Rare Case Series

Abstract

INTRODUCTION: Linear morphea is rare localized form of scleroderma. The lesions are characterized by localized hard/smooth ivory-coloured immobile areas of skin. The appearance is hidebound skin, known as andrew's disease of skin. These linear lesions often develop along the line of blaschko. METHOD: A cross-sectional,hospital-based clinical study of patients with linear morphea attending the Outpatient Department of tertiary care centre was done over a span of 3 months. Detailed history was taken along with clinical examination. After counselling and after recording their consent, skin biopsy done along with routine investigations and results were evaluated. RESULTS: We have come across six cases in 3 months. Age group ranged from 10-20 years with 2 male and 4 female patients. Average age of onset was 14.5 years. Two cases had lesions involving limbs, two had lesions on forehead and one patient had extensive lesions involving entire right half of body including face. Serum ANA titre was positive in one case,which also showed changes in CT scan and bone scan. EEG changes were seen in two out of three cases of facial lesions. Skin biopsy in all cases were consistent with morphea. CONCLUSION: Though linear morphea is a local disorder without systemic association generally,patients with Serum ANA positivity and EEG changes in facial lesions need to be observed for permanent CNS damage if not counteracted with immunosuppressives. As it has higher morbidity and predilection in younger population,cosmetic and functional disability caused by it affects the quality of life.