A female neonate, born after a gestation of 38 weeks and 6 days, received a diagnosis of ductal shock at the age of 2 days, along with vascular ring with right-sided interrupted aortic arch, right-sided descending aorta, right-sided patent ductus arteriosus, severe valvular aortic stenosis, and ventricular septal defect. At 3 days of age, the infant underwent bilateral pulmonary artery banding. At the age of 3 months and 29 days, she underwent a Norwood-type operation and release of the vascular ring. At age 23 months, she underwent a Rastelli-type operation. Successful surgical repair of this anomaly has yet not been reported.