Left Main Coronary Atresia

Abstract

Left main coronary artery atresia (LMCAA) is one of the least frequently observed congenital coronary anomalies. We describe a case series of LMCAA, highlighting the clinical presentation, characteristic, and treatment.

Congenital Ostial Atresia of the Left Anterior Descending Artery

“…1,2 Congenital atresia of the LMCA is a very rare disease, and only a small number of reports have been published. 3 In the present case, the absence of aortitis, Kawasaki disease history, calcium deposits, arteriosclerosis, and of continuity between the LMCA and the proximal tip of the LAD suggested a congenital phenotype. Furthermore, on CTA the LAD was occluded, with no evidence of ostial stamp of the LAD distal tip, and the proximal tip of the LAD seemed to approach the main pulmonary artery while leaving a trabecular trace.…”

Unusual congenital coronary artery anomaly in a young adult presenting as sudden cardiac arrest

“…The left coronary circulation is supplied by the RCA through collaterals. In paediatric patients, LMCAA usually coexists with other cardiac abnormalities such as valvular disease with the onset of symptoms early in life 4. In adults, LMCAA can be found in isolation and is usually asymptomatic early in adult life 5.…”

A Rare Case of Left Main Coronary Artery Atresia

“…The overall incidence is estimated between 0.6% and 1.3% [1][2][3]. A recent review found a total of only 53 cases of LMCA atresia ever reported in the literature, including both pediatric and adult cases [3]. The authors found more than half of the patients survived into adulthood with a presentation of either angina or atypical chest pain.…”

“…In fact, left main coronary artery (LMCA) atresia remains one of the least frequently observed variations. The overall incidence is estimated between 0.6% and 1.3% [1][2][3]. A recent review found a total of only 53 cases of LMCA atresia ever reported in the literature, including both pediatric and adult cases [3].…”