Late Infantile Neuronal Ceroid Lipofuscinosis in a Tunisian Boy

Cataract and Glaucoma Development in Juvenile Neuronal Ceroid Lipofuscinosis (Batten Disease)

“…Similarly, no anterior segment abnormalities were reported among 25 children with late infantile NCL regardless of the severity of the retinal degeneration. 10 However, the anecdotally reported posterior polar cataract in infantile 7 and late infantile NCL, 8 and the results from the present study demonstrate that anterior segment abnormalities such as cataracts do occur in Batten disease and constitute a problem due to the potential risk of developing acute glaucoma.…”

“…4 Interesting to note, however, is the anecdotally reported posterior polar cataract in infantile 7 and late infantile NCL. 8 In the present study we report the findings of pre-senile cataract in five Danish patients with JNCL.…”