Klippel-Trenaunay-Weber Syndrome: A clinical case report

Silva, Mirian Azevedo Pereira da; Melo, Marcelo Rodrigo Vaz de; Villalobos, Maria Isabel de Oliveira e Britto; Cardoso, Cláudia Assunção e Alves; Valerio, Claudia Scigliano; Manzi, Flávio Ricardo

doi:10.1016/j.pdj.2017.11.001

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2023

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Cited by 2 publications

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“…In the orofacial region, the affected patients may present with haemangioma (naevus flammeus), early tooth eruption, gingival hyperplasia, hypertrophy of soft tissue such as enlarged lip, cheek, and tongue, and jawbone hypertrophy causing asymmetry, malocclusion and anterior open bite. In addition, haemangioma of the oral mucosa limited to the affected side has been noticed [ 1 , 3 , 4 ].…”

Section: Introductionmentioning

confidence: 99%

Klippel-Trenaunay-Weber syndrome: Oro-dental manifestations and management

Daume,

Renz,

Trento

et al. 2023

International Journal of Surgery Case Reports

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Section: Introductionmentioning

confidence: 99%

Klippel-Trenaunay-Weber syndrome: Oro-dental manifestations and management

Daume,

Renz,

Trento

et al. 2023

International Journal of Surgery Case Reports

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“…In addition, haemangioma of the oral mucosa limited to the affected side has been noticed. 1,3,4 The objective of this study is to present a case of an adult patient, who was diagnosed with KTWS in his childhood, giving special attention to the oral and maxillofacial treatment and its possible complications.…”

Section: Introductionmentioning

confidence: 99%

Klippel-Trenaunay-Weber syndrome: oro-dental manifestations and management

Daume

Renz

Trento

et al. 2023

Preprint

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Background: Klippel-Trenaunay-Weber syndrome (KTWS) is a rare congenital systemic disease characterized by cutaneous haemangioma, arterio-venous fistulas or varicosities (or both) and unilateral hypertrophy of hard and soft tissue with different localizations. Typical orofacial manifestations include facial asymmetry, jaw enlargement and malocclusion. Case presentation: A previously diagnosed 55-year-old male patient was referred to the Department of Cranio-Maxillofacial Surgery presenting with extended mandibular ramus exostosis on the left side and concomitant malocclusion. Surgical removal of the hypertrophic bone was performed due to progressive mouth opening restriction, limited oral hygiene ability and increased mandible deviation. Bleeding complications and wound healing disorders were not observed. Consistent mouth opening training resulted in an improvement in mouth opening. Conclusion: It is suggested to consider KTWS as one of the differential diagnoses if vascular syndromes in the head and neck region occur. Special attention must be given to dental treatment due to eventual excessive haemorrhage that might occur after oral surgical procedures.

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Klippel-Trenaunay-Weber Syndrome: A clinical case report

Cited by 2 publications

References 10 publications

Klippel-Trenaunay-Weber syndrome: Oro-dental manifestations and management

Klippel-Trenaunay-Weber syndrome: Oro-dental manifestations and management

Klippel-Trenaunay-Weber syndrome: oro-dental manifestations and management

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