Isolated pulmonary vasculitis: Case report and literature review

Riancho‐Zarrabeitia, Leyre; Zurbano, Felipe; Gómez-Román, Javier; Martínez-Meñaca, Amaya; López, Marta Reyero; Hernández-Hernández, Miguel A.; Pina, Trinitario

doi:10.1016/j.semarthrit.2014.10.003

Cited by 15 publications

(18 citation statements)

References 19 publications

(18 reference statements)

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“…LB is required in up to 30% of interstitial pulmonary processes for diagnosis [7]. However, due to its potential risks, particularly in patients with respiratory compromise or pulmonary hypertension, its indication should be very thoughtfully considered [8,9].…”

Section: Discussionmentioning

confidence: 99%

Anti-Neutrophil Cytoplasmic Antibody (Anca)-Negative Small Vessel Pulmonary Vasculitis in a Chronic Hemodialysis Patient

Merino¹

2016

J Clin Nephrol Ren Care

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The development of vasculitis in renal replacement therapy is rare due to the immunological condition of these patients. Its diagnosis is often complex and invasive tests are usually required. A multidisciplinary approach is mandatory and a broad study (including lung biopsy) is necessary for its diagnosis which is crucial to support the necessity of immunosuppressive therapy in this kind of patients. We report a case of a hemodialysis patient with anti-neutrophil cytoplasmic antibody (ANCA)-negative small vessel pulmonary vasculitis de novo diagnosed two years after starting dialysis.

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Section: Discussionmentioning

confidence: 99%

Anti-Neutrophil Cytoplasmic Antibody (Anca)-Negative Small Vessel Pulmonary Vasculitis in a Chronic Hemodialysis Patient

Merino¹

2016

J Clin Nephrol Ren Care

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“…In the first of their cases, despite surgery and medical treatment for the vasculitis, some of the pulmonary arteries remained occluded and narrowed. Isolated pulmonary vasculitis has also been described as rare causes of pulmonary hypertension and pulmonary artery aneurysms 7 8…”

Section: Discussionmentioning

confidence: 99%

Pulmonary vasculitis mimicking chronic thromboembolic disease

et al. 2019

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A 29-year-old female patient presented with chest pain, breathlessness and syncope on the background of constitutional symptoms, oral ulceration and a rash. Multiple investigations were performed, including a CT pulmonary angiogram (CTPA) that was initially felt to show imaging features consistent with a diagnosis of chronic thromboembolic disease (CTED). The patient was referred to a tertiary pulmonary hypertension centre and the possibility of pulmonary vasculitis was raised. Subsequent positron emission tomography (PET)-CT revealed imaging features supporting this diagnosis. The patient was treated with intravenous cyclophosphamide infusions, following which her symptoms improved. A repeat PET-CT 6 months after treatment showed resolution in pulmonary artery and mediastinal uptake, but persistence of pulmonary artery occlusions on a repeat CTPA. A final diagnosis of pulmonary vasculitis secondary to Behçet’s disease was made. This case report aims to raise awareness of the imaging features of CTED and its mimics.

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“… 15 , 16 Isolated pulmonary vasculitis has only been reported in a few case reports. 17 – 19 Hagan et al. described two patients with isolated large-vessel pulmonary vasculitis who displayed chronic obstruction of pulmonary arteries as opposed to aneurysmal dilatation, and underwent pulmonary endarterectomy in addition to pharmacological immunosuppression.…”

Section: Discussionmentioning

confidence: 99%

“… 17 In two other reports, the patients presented with pulmonary arterial hypertension secondary to localized pulmonary vasculitis involving the medium-sized vessels. 18 , 19 Both patients failed immunosuppressive therapy and were offered bilateral lung transplantation. Unlike our patient, in most of the reported cases significant respiratory symptoms with elevated inflammatory markers were observed.…”

Section: Discussionmentioning

confidence: 99%

Isolated large vessel pulmonary vasculitis leading to pulmonary artery aneurysm formation: a case report and literature review

Moghaddam

Dehghan

et al. 2018

Pulm. circ.

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Pulmonary artery (PA) vasculitis occurs in association with primary vasculitides—in particular, giant cell arteritis, Takayasu’s arteritis, or Behçet’s disease—or secondary vasculitis as a result of infections or malignancy. However, PA vasculitis in isolation and with concomitant aneurysmal dilation is an unusual finding. We present a rare case of PA aneurysm secondary to isolated PA vasculitis in an asymptomatic patient with no features of systemic vasculitis. This case highlights one of the first cases of PA vasculitis managed with surgical resection alone.

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Isolated pulmonary vasculitis: Case report and literature review

Cited by 15 publications

References 19 publications

Anti-Neutrophil Cytoplasmic Antibody (Anca)-Negative Small Vessel Pulmonary Vasculitis in a Chronic Hemodialysis Patient

Anti-Neutrophil Cytoplasmic Antibody (Anca)-Negative Small Vessel Pulmonary Vasculitis in a Chronic Hemodialysis Patient

Pulmonary vasculitis mimicking chronic thromboembolic disease

Isolated large vessel pulmonary vasculitis leading to pulmonary artery aneurysm formation: a case report and literature review

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