Intra and extra-hepatic cystadenoma of the biliary duct. Review of literature and radiological and pathological characteristics of a very rare case

Soochan, Diana; Keough, Valerie; Wanless, Ian R.; Molinari, Michele

doi:10.1136/bcr.01.2012.5497

Cited by 26 publications

(30 citation statements)

References 17 publications

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“…(2, 5-10) The mean age at presentation of BCA is 45 years versus BCAC which typically presents a decade later. (7-11) While 10% of reported BCT originate in the extrahepatic biliary tree, the overwhelming majority arises from the intrahepatic biliary system. (12-15) BCT are typically slow growing lesions with a reported size that can range in diameter from 1.5 to 35 cm.…”

Section: Incidence and Epidemiologymentioning

confidence: 99%

“…Many patients with BCT will be asymptomatic; other patients with BCT can present with non-specific symptoms, most commonly abdominal pain and distention (55-90%). (3, 7, 11, 17, 18, 23) While laboratory values are normal in most patients, approximately 20% of patients present with elevated liver function tests such as an abnormal bilirubin level. (19, 24) Obstructive jaundice and cholangitis are rare and do not correlate with malignant disease and typically occur with extrahepatic BCT.…”

Section: Presentation and Differential Diagnosis Considerationsmentioning

confidence: 99%

“…(11, 24) Biliary IPMN is a recently recognized entity characterized by mucin production and prominent intraductal papillary proliferation. (34, 35) Biliary IPMN occurs equally in both genders with a mean age of 58 years.…”

Section: Presentation and Differential Diagnosis Considerationsmentioning

confidence: 99%

See 2 more Smart Citations

Cystic Neoplasms of the Liver: Biliary Cystadenoma and Cystadenocarcinoma

Soares

Arnaoutakis

Kamel

et al. 2014

Journal of the American College of Surgeons

152

138

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Section: Incidence and Epidemiologymentioning

confidence: 99%

Section: Presentation and Differential Diagnosis Considerationsmentioning

confidence: 99%

See 1 more Smart Citation

Cystic Neoplasms of the Liver: Biliary Cystadenoma and Cystadenocarcinoma

Soares

Arnaoutakis

Kamel

et al. 2014

Journal of the American College of Surgeons

152

138

View full text Add to dashboard Cite

“…[2][3][4][5][6] It accounts for less than 5% of nonparasitic hepatic cystic lesions. It was first described in 1943 and, to date, less than 200 cases have been reported.…”

Section: Discussionmentioning

confidence: 99%

Extrahepatic Biliary Cystadenoma: A Rare Cause of Biliary Obstruction

Metussin¹,

Telisinghe²,

Kok³

et al. 2015

Oman Med J

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Biliary cystadenoma is a rare tumor of the biliary tree and a rare cause of obstructive jaundice. Most are intrahepatic, and pure extrahepatic biliary cystadenoma is less common. Cases are more common in women. Unless suspected, diagnosis of extrahepatic biliary cystadenoma is often delayed. Here, we report the case of a young woman with extrahepatic biliary cystadenoma who presented at Raja Isteri Pengiran Anak Saleha Hospital with obstructive jaundice initially thought to be due to a large biliary stone based on the endoscopic cholangiogram image. She was successfully managed with resection of the cystadenoma.

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“…Biliary cystadenoma involving the extra- and intrahepatic bile ducts simultaneously is less frequent. To our knowledge, there has been one published case [5] that describes a biliary cystadenoma involving the intrahepatic duct extending to the common bile duct. We aim to highlight here an instance of biliary cystadenoma involving the intra- and extrahepatic bile ducts, which is an uncommon presentation.…”

Section: Introductionmentioning

confidence: 99%

Filling Defect on ERCP: Biliary Cystadenoma, a Rare Tumor

Rayapudi

Schmitt

Olyaee

2013

Case Rep Gastroenterol

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Biliary cystadenomas are rare tumors of the bile ducts most commonly presenting as large right liver lobe lesions. These are usually slow-growing and mostly benign. They commonly present with abdominal pain. On physical exam an abdominal mass can be identified occasionally. Walls of biliary cystadenomas appear thicker than simple cysts, with soft tissue nodules and enhancing septations on CT or MRI. Radiographic images can vary with the amount of protein content in the fluid on CT or MRI. Due to the risk of malignant transformation, complete surgical resection is advised. Hereby, we describe a 37-year-old lady who presented to the outpatient clinic with bloating and abdominal discomfort with intermittent elevated liver enzymes and hyperbilirubinemia. Ultrasound of the liver and bile ducts followed by CT scan and magnetic resonance cholangiopancreatography confirmed the presence of biliary cystadenoma of the intra- and extrahepatic ducts. It was seen as a filling defect of the intra- and extrahepatic ducts (common hepatic duct) on endoscopic retrograde cholangiopancreatography. Involvement of the intra- and extrahepatic bile ducts simultaneously is a rare presentation of this tumor. She later on underwent exploratory laparotomy with extrahepatic bile duct resection, left hepatic lobe resection and reconstruction with hepaticojejunostomy. Pathology confirmed the presence of biliary cystadenoma with ovarian-like stroma. She had recovered uneventfully from the surgery when seen 2 weeks later in the clinic. Biliary cystadenoma is a rare, mostly benign neoplasm of the biliary tract that should be considered in the differential diagnosis of cystic lesions of the biliary tract.

show abstract

Intra and extra-hepatic cystadenoma of the biliary duct. Review of literature and radiological and pathological characteristics of a very rare case

Cited by 26 publications

References 17 publications

Cystic Neoplasms of the Liver: Biliary Cystadenoma and Cystadenocarcinoma

Cystic Neoplasms of the Liver: Biliary Cystadenoma and Cystadenocarcinoma

Extrahepatic Biliary Cystadenoma: A Rare Cause of Biliary Obstruction

Filling Defect on ERCP: Biliary Cystadenoma, a Rare Tumor

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