Intra-Abdominal Pulmonary Sequestration: A Case Report and Literature Review

Abstract

Pulmonary sequestration is a rare congenital malformation mostly located in the thorax, while intra-abdominal pulmonary sequestration is an extremely rare type of pulmonary sequestration usually diagnosed during the first 6 months of life. Only 1 case of intra-abdominal pulmonary sequestration in a patient older than 60 years has been reported in the current literature. It is difficult to differentiate an intra-abdominal pulmonary sequestration from other retroperitoneal tumors. A definitive diagnosis is always made by histologi- cal examination. Intra-abdominal pulmonary sequestration commonly responds well to surgical resection and is associated with excellent results and prognosis. The authors present the case of a 74-year-old asymptomatic man with a retroperitoneal mass which was completely excised and revealed by histopathological study to be an intra-abdominal pulmonary sequestration.

Surgical management of adrenal cysts: a single-institution experience

“…Bronchogenic cyst is a rare developmental abnormality of the primitive foregut that arises during early embryogenesis from abnormal budding of the developing tracheobronchial tree (23). Pulmonary sequestration cyst is extremely rare and is characterized by a mass of nonfunctional lung tissue without communication with the bronchopulmonary tree and fed from an aberrant systemic artery (24). In both bronchogenic cyst and pulmonary sequestration cyst, histology still remains the routine method of diagnosis and surgery remains the predominant therapeutic option (23,24).…”

Extralobar pulmonary sequestration: A case report and literature review

“…The incidence of PS in congenital malformation of the lung is 1.1%–1.8% 1 . ELS can occur in the thoracic cavity, mediastinum, pericardium, and intra‐ or sub‐diaphragm, 3 and the retroperitoneal ELS of the 33‐year‐old man mentioned in this case is even rarer, with only 10%–15% of ELS being found in retroperitoneal sites 4 …”

“…The pathogenesis of pulmonary sequestration (PS) is unclear and is currently considered to be common with the parapneumonic bud theory, the traction theory, and vascular development theory, but the parapneumonic bud theory is currently recognized, which anatomically classifies pulmonary sequestration into two types (Figure 1), intralobar pulmonary sequestration (ILS) and extralobar pulmonary sequestration (ELS), based on the relationship between the mass and the pleural covering. 1 PS arises from the primitive foregut, if the pulmonary bud develops before the pleura and is covered by adjacent lung tissue, ILS is present and if this pulmonary bud develops later than the pleural development and grows independently, it results in ELS. 2 The incidence of PS in congenital malformation of the lung is 1.1%-1.8%.…”

An unusual case of extrapulmonary sequestration presenting as vomiting in a neonate

“…Pulmonary sequestration is a rare and mostly sporadic congenital malformation with an incidence of 0�1-6% of all congenital lung malformations� There are two distinct forms of pulmonary sequestrations: intralobar and extralobar, depending on whether it has independent pleura and its location of within the lobe of lung or outside lobes of the lung� [1][2][3] This article presents a case of extralobar pulmonary sequestration that presented with incessant vomiting and inability to take feeds in a 16-day-old female� The extralobar pulmonary sequestration was in a rare transdiaphragmatic location�…”