Infected Intradural Dermoid Cyst with Complete Dermal Sinus of Posterior Fossa

Intradural dermoid cyst with complete dermal sinus of the posterior fossa: Contribution of 3D imaging with histopathological correlation

“…We report imaging findings of a complete dermal sinus associated with an infected intradural dermoid cyst with histopathological correlation, and to the best of our knowledge, only a few case reports have correlated imaging findings with histopathology [7 , 8] .…”

“…They are classified into four categories depending on the status of the occipital dermal sinus: (1) an extradural dermoid cyst with a complete dermal sinus; (2) an intradural dermoid cyst with no dermal sinus; (3) an intradural dermoid cyst with an incomplete dermal sinus; and (4) an intradural dermoid cyst with a complete dermal sinus [9] . This is related to the embryology of the falx and tentorium, presumably resulting from ectodermal fragments being pulled in during the invagination of the dural folds [7 , 9] . Infratentorial dermoid cysts may retain their attachment to the skin through a persistent narrow dermal sinus through an occipital bone defect, unlike those located in the supratentorial area.…”

Senos dérmicos craneales en pediatría: presentación, diagnóstico, complicaciones y tratamiento. Experiencia de un hospital pediátrico de nivel III

“…En estos últimos, es más frecuente encontrar síntomas infecciosos que pueden variar desde enrojecimiento del defecto a meningitis fulminante. 13,14 La mitad de los pacientes de este estudio, presentaron signos de infección y más de la mitad presentaron una lesión intracraneana asociada, cuyos síntomas predominantes fueron infecciosos en la mitad de los casos, seguido por síntomas de hipertensión endocraneana, ataxia y fístula por la herida.…”

“…El 82 % se extienden hacia el espacio subdural o más profundo y el 18 % son puramente extradurales. [12][13][14][15] El diagnóstico de estas lesiones se realiza por estudios por imágenes como la RM y la TC. La información más importante que se debe extraer de estos estudios es la extensión del seno dérmico y si se acompaña o no de una lesión extracraneana o intracraneana.…”

Congenital Dermal Sinus: case series and the consequences of late diagnosis and treatment

“…Although considered a benign lesion that presents with normal neurological status at birth, in about half of patients complications such as meningitis, abscess, osteomyelitis, rupture of an associated epi/dermoid cyst, can be the first symptom, as we showed in the 3 cases presented, and even lead to permanent deficits and even death. Chances are higher in older ages (3,6,9,11). For that reason, once suspected, a further investigation should include ultrasonography (if in the lumbar region and before 3 months of age), CTscan(thin slices) and/or MRI, as well a neurosurgical consultation for complete resection, the treatment of choice (7,8).…”