Incidental leiomyosarcoma within an ischaemic gut: a review of the management of visceral sarcoma

Abstract

Leiomyosarcomas are rare, primary malignancies that can be found in the small bowel in a minority of cases. The management of these visceral sarcomas remains controversial, with surgical resection forming the mainstay, being optimally achieved in a unit familiar with the management of sarcomas. These tumours are difficult to diagnose based on history and are challenging to localize on conventional imaging modalities. We report a case of a 61-year-old female who proceeded to emergent laparotomy with imaging suggestive of small bowel ischaemia secondary to portal venous thrombosis. Incidental leiomyosarcoma was noted on histology and was discussed at local multidisciplinary meeting regarding further management.

A Rare Case of Leiomyosarcoma Arising From the Stomach: A Case Report and Review of the Literature

“…Risk factors for LMS include a prior history of radiotherapy, genetic syndromes including hereditary retinoblastoma and Li-Fraumeni syndrome, and Tamoxifen use [1,[4][5]. Patients suffering from gastrointestinal LMS typically present with abdominal pain or discomfort, bloating, unintentional weight loss, changes in bowel habits, symptomatic and incidental anemia, and gross or occult gastrointestinal bleeding [3,6].…”