Incidental Finding of Congenital Unilateral Pulmonary Vein Atresia During Work-Up for Non-Specific Chest Pain

Right Sub-axillary Incision for Right Pulmonary Vein Atresia in a Child: A Case Report and Literature Review

“…Patients usually show different degrees of clinical signs and symptoms, ranging from repeated pulmonary infection, exertional dyspnea, and hemoptysis to no symptoms at all. Pulmonary hypertension may occur in only some patients, and a case report from the United States was the first to report that a 16-year-old patient did not have concurrent pulmonary hypertension [7] . The initial symptoms of UPVA are easily misdiagnosed as tuberculosis or secondary malignant tumors of the lung.…”

“…Hemoptysis is caused by the rupture of bronchial varices or the systemic and pulmonary collaterals, which often indicates that the condition is serious and there is a higher possibility of resection of the affected lung. Some patients may not have obvious clinical signs or symptoms, and only occasional chest pain in a patient can allow for a definite diagnosis [7] .…”

“…At present, there are no clear treatment guidelines or mature treatment plans. It has been reported that some patients had no obvious symptoms and were followed up for a long time [1,7,8] . If the patient has repeated pulmonary infections and hemoptysis and is older at the time of diagnosis, pneumonectomy on the affected side is helpful to improve the quality of life [4,10] .…”