“…The mainstays of a wide array 6 of daily therapies are chest physiotherapy, regular courses of antibiotics and pancreatic enzymes, with patients attending specialist centres for paediatric and adult care reported to achieve a better clinical outcome (Mahadeva et al, 1998). Survival age has steadily increased from under one year in the late 1930s (Anderson, 1938) to 31.5 years currently (Dodge et al, 1997), as the disease is better understood and treatment and care are developed. Adults are generally knowledgeable about their disease and treatment and most have well-established relationships with healthcare staff.…”