“…There are few reports in head and brain involvements of IgG4-RD in the form of hypertrophic pachymeningitis, cranial nerve impairments, pituitary gland inflammatory lesions, orbital pseudotumor, pterygopalatine fossa infiltrations, and recently central nervous system (CNS) parenchymal involvement [6][7][8][9] . Hypertrophic pachymeningitis characterized by dura matter inflammation in the periorbital areas, clivus, vestibular structures, brainstem, and spinal nerve roots and usually presents with focal neurological signs and symptoms 10 .…”