Imaging Appearance of Renal Epithelioid Angiomyolipoma: a Rare Variant of Renal Angiomyolipoma with Diverse Clinical Behaviours

Abstract

Renal epithelioid angiomyolipoma is a rare variant of renal angiomyolipoma. The condition occurs in patients with or without tuberous sclerosis. Clinical behaviour of renal epithelioid angiomyolipoma varies widely, ranging from benign to malignant. Only a few reports have described its radiological features. We report two cases of renal epithelioid angiomyolipoma in patients without tuberous sclerosis. The first patient had no recurrence after nephrectomy, while the other patient had metastasis at presentation and initially responded to temsirolimus but later showed disease progression.