“…Subsequently, multiple similar cases were described, and different names have been used, including intraepidermal neutrophilic IgA dermatosis (2–4); atypical neutrophilic dermatosis (5); intercellular IgA dermatosis (6); intercellular IgA vesiculopustular dermatosis (7); IgA herpetiform pemphigus (8) and IgA pemphigus foliaceus (9). The term “IgA Pemphigus” has been more often used since it was first proposed by Hodak et al (10) and Caputo et al (11) IgA pemphigus is a newly characterized group of autoimmune, intraepidermal, blistering diseases that exhibit a vesiculopustular eruption, neutrophil infiltration, acantholysis, and in vivo bound and circulating IgA autoantibodies that target cell surface components of the epidermis (12). Currently, IgA pemphigus has been classified into two distinct subtypes: subcorneal pustular dermatosis (SPD type) (1, 2, 5, 6, 10, 12, 19–27, 29–33, 35–39) and intraepidermal neutrophilic IgA dermatosis (IEN type) (3, 4, 6, 12, 14, 18–21, 27, 28, 33, 34, 38).…”