Idiopathic Retroperitoneal Fibrosis

Sakai, Yasuhiro; Nasu, Tsuyoshi

doi:10.1111/j.1440-1827.1976.tb00521.x

Cited by 4 publications

(2 citation statements)

References 21 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Fibrosing mesenteritis is rare benign process that involves inflammation, fat necrosis, and fibrosis of the mesentery [ 34 ] has been also reported to cause CA [ 17 ]. Other rare inflammatory causes include idiopathic retroperitoneal fibrosis, [ 35 ] sarcoidosis, [ 36 ] systemic lupus erythematous, [ 37 ] peritoneal dialysis, [ 38 ] and hyperthyroidism [ 39 ].…”

Section: Etiologymentioning

confidence: 99%

Chylous Ascites: Evaluation and Management

et al. 2014

View full text Add to dashboard Cite

Chylous ascites refers to the accumulation of lipid-rich lymph in the peritoneal cavity due to disruption of the lymphatic system secondary to traumatic injury or obstruction. Worldwide, abdominal malignancy, cirrhosis, and tuberculosis are the commonest causes of CA in adults, the latter being most prevalent in developing countries, whereas congenital abnormalities of the lymphatic system and trauma are commonest in children. The presence of a milky, creamy appearing ascitic fluid with triglyceride content above 200 mg/dL is diagnostic, and, in the majority of cases, unless there is a strong suspicion of malignancy, further investigations are not required in patients with cirrhosis. If an underlying cause is identified, targeted therapy is possible, but most cases will be treated conservatively, with dietary support including high-protein and low-fat diets supplemented with medium-chain triglycerides, therapeutic paracentesis, total parenteral nutrition, and somatostatins. Rarely, resistant cases have been treated by transjugular intrahepatic portosystemic shunt, surgical exploration, or peritoneovenous shunt.

show abstract

Section: Etiologymentioning

confidence: 99%

Chylous Ascites: Evaluation and Management

et al. 2014

View full text Add to dashboard Cite

show abstract

“…One case report in the literature reports chylous ascites occurring once during the course of progressive idiopathic RPF. 3 To our knowledge, ours is the first case report that describes chylous ascites as an initial presentation of underlying RPF. Chylous ascites frequently presents as a progressive and painless abdominal distension, particularly if due to an atraumatic cause.…”

Section: Discussionmentioning

confidence: 66%

Retroperitoneal Fibrosis as a Cause of Chylous Ascites

Rahman

Ramaraj

Humphreys

et al. 2017

ACG Case Reports Journal

View full text Add to dashboard Cite

Retroperitoneal fibrosis is a rare condition characterized by chronic inflammation and marked fibrosis of the retroperitoneal tissue, often leading to entrapment of abdominal organs. We report a 69-year-old white man who presented with a 5-week history of gradual onset of progressive abdominal distension. He had no history or risk factors for an underlying liver condition. Ascites and a retroperitoneal mass encasing the major abdominal vessels were revealed on imaging. Biopsies of the mass confirmed the presence of retroperitoneal fibrosis, and the ascitic fluid was milky, consistent with chylous ascites. We discuss this rare presentation and the challenges of treatment for chylous ascites caused by RPF, including the role for supportive treatment.

show abstract

Retroperitoneal fibrosis associated with scirrhous gastric cancer

et al. 1993

View full text Add to dashboard Cite

A case of retroperitoneal fibrosis associated with scirrhous gastric cancer is reported. A sixty two-year-old Japanese female was admitted because of acute renal failure. The patient's serum creatinine level showed 3.2 mg/dl while the blood urea nitrogen level was 23 mg/dl. An ultrasound study of the upper abdomen revealed bilateral hydronephrosis. Drip infusion pyelography revealed a dilated right renal pelvis without ureteral obstruction. The left kidney was not opacified, suggesting a functional disorder. Gastrography and gastrofiberscopy revealed scirrhous gastric cancer. Signet ring cell carcinoma was later demonstrated histologically by biopsy specimens. CT demonstrated a prominent thickening of the gastric wall and hydronephrosis, although no prevertebral soft tissue masses were observed. A total gastrectomy was performed with failure to surgically decompress the ureters because fibrous plaque had firmly enveloped the retroperitoneal structures. Biopsy specimens of the retroperitoneum revealed an invasion of the tumor cells and prominent fibrosis. As an etiology of renal failure, ureteral stenosis resulting from secondary retroperitoneal fibrosis was also considered.

show abstract

Idiopathic Retroperitoneal Fibrosis

Cited by 4 publications

References 21 publications

Chylous Ascites: Evaluation and Management

Chylous Ascites: Evaluation and Management

Retroperitoneal Fibrosis as a Cause of Chylous Ascites

Retroperitoneal fibrosis associated with scirrhous gastric cancer

Contact Info

Product

Resources

About