Idiopathic Cutis Verticis Gyrata in a Female

Abstract

Cutis verticis gyrata (CVG) is a benign proliferation and hypertrophy involving the scalp which exhibits furrows resembling the cerebral cortex convolutions. The diagnosis of CVG is based on clinical findings. Complementary investigations are recommended to rule out local or systemic underlying disorders.Idiopathic or essential primary CVG refers to cases without obvious origin and with no other associated abnormalities. These forms affect mainly men. Herein, the authors present a new observation of an idiopathic CVG in a female, which seems to be extremely rare.

Inmate carrier of cutis verticis gyrata

“…To categorise the CVG for prognostic and therapeutic purposes, the following additional diagnostic tests and consultations were programmed, based on the recommendations of other authors [1][2][3][4][5][6][7][8]…”

“…The question was again asked if he noticed lumps or ridges when he had long hair, or if the scalp bothered him or itched, since these symptoms are common in CVG 1,2,6 . He said that ha was not aware of having any lesions, and this time he admitted that he had shaved his head 5 or 6 years previously and that then there was no visible anomaly.…”

“…The extent, shape and thickness may vary and it appears in the parietal and occipital areas of the scalp. The skin and subcutaneous tissue of the cranium thicken and copy the shape of the brain surface, which is why it has received other names, now no longer used, such as pachydermie vorticellee, cerebriform deformity, cutis sulcata, bulldog scalp or cutis capitis strata [1][2][3][4][5][6][7][8] .…”

“…The aetiology is considered to be idiopathic or essential (CVG primary essential) when it is not associated with any other pathology [2][3][4][5] . In such essential cases, no malignant disruption has been reported, and the only problem may be an aesthetic one.…”

“…The cases of CVG primary non essential are much more frequent and are the ones associated with neurological and ophthalmologic conditions, especially severe mental retardation, intracranial brain disorders, convulsions, cerebral palsy, strabismus, cataracts or blindness 1,3,8 . Finally, the cases of CVG secondary (occasionally reversible) have not been very well clarified and have become a "catch all", where there is confusion between associations and different causes (pachydermoperiostosis, cerebriform intradermal nevus, liver disorders, hamartomas, neurofibromas, dermatosis of the scalp, psoriasis, tumours, hypergammaglobulinemia inmunoglobulina E (IgE), endocrine disruption, syphilis, acromegalia, amiloidosis, cretinism, diabetes mellitus, fragile X chromosome syndrome, Ehlers-Danlos syndrome, Graves' disease, Turner's syndrome and a wide range of chromosome disorders [1][2][3][4][5][6][7][8] . This study reports the first case of a patient carrying CVG in prison.…”