Ann RC oll Surg Engl 2009; 91:5 32-534 532Bleeding per urethram is ac ommon urological symptom which prompts urgent investigation, aimed primarily at excluding malignancy.T he differential diagnosis in these patients is considerable. We present three cases of urethral bleeding associated with post-coital ejaculation that was found to be caused by urethral venous malformations, a condition that is rare but probably under-reported.
Patients and MethodsThe case notesofthree patients who wereidentified as suffering from post-coital urethral bleeding were reviewed. Due to the rarity of the disease and the lack of standardisation in the diagnosisa nd treatment, personal communication withe ach surgeon was necessary for am ore accurate descriptiono ft he intra-operativefindings and details of the surgical treatment. A search and reviewo ft he literature publishedi nE nglish was performed using the PubMed database.
ResultsThe three patients in this series were treated by three different urological surgeons, all practising in the same unit. Cases are reported both separately and in comparison (Table 1).
Case report 1A5 8-year-old man represented to the department of urology in 2007 with ah istory of haematospermia and haematuria spanning 20 years. The patient reported that episodes of haematospermia and haematuria were provoked by ejaculation. He was first investigated for frank haematuria 18 years previously when it was reported that there was no abnormality of the urinary tract. He was re-investigated for haematuria 10 years later when large 'varicose veins' were noted in the bulbar and membranous urethra, coursing over the external sphincter muscle. Three years previously, he was again referred complaining of haematuria. On this occasion, af lexible cystoscopy was reported as normal. Over the next 2y ears, the patient was admitted to hospital on three occasions with further episodes of heavy haematuria and the passage of clots. Investigations including an intravenous urogram, renal/pelvic ultrasound scan and magnetic resonance imaging (MRI) of the pelvis were reported as normal. His most recent cystourethroscopy, however,demonstrated large, abnormal branching veins in the bulbar urethra (Fig. 1) on either side of the verumontanum and around the bladder neck. In addition, within the bladder there were abnormal sub-mucosal veins high on the posterior bladder wall. Judicious 'spot-welding' of these veins at the bladder neck, alongside the verumontanum and in the bulbar urethra was performed using diathermy coagulation. At 6-month review,t he patient was free of postcoital haematospermia and haematuria for the first time in 20 years.
Case report 2A4 1-year-old man was referred with a1 0-year history of intermittent haematuria with clots. This had always been associated with sexual activity and ejaculation. There was
CASE REPORTS