Hypohydrotic Ectodermal Dysplasia: A Clinical Case

Abstract

Ectodermal dysplasia is a rare inherited disorder distinguished by the not normal development of certain structures of ectodermal origin. The hypohydrotic ectodermal dysplasia has an autosomal recessive or X-linked inheritance, the latter being the most frequent. Patients with ectodermal dysplasia are patients who require a multidisciplinary approach to their treatment. It is of great importance that the patient is treated at an early age so that their self-esteem and their integration into society are not affected. Due to the oral characteristics of the DEH, the most common treatment is the elaboration of total prostheses, although the clinician may face various difficulties such as the poor development of alveolar processes and dry mouth, resulting from the poor or no salivary secretion.