Hughes-Stovin Syndrome Presenting With Hematuria

Jambeih, Rami; Salem, George J.; Huard, David; Jones, Kellie; Awab, Ahmed

doi:10.1097/maj.0000000000000571

Cited by 8 publications

(11 citation statements)

References 6 publications

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“…Few articles reported cases of Hughes Stovin Syndrome revealing BD. It's a rare entity defined as thrombophlebitis associated with pulmonary aneurysms [15]. Few cases were reported with associated aneurysm of the systemic circulation such bronchial, external carotid, iliac artery aneurysm and left hepatic artery [16] but no association with ascending aorta aneurysm was reported.…”

Section: Discussionmentioning

confidence: 99%

Cardiac and vascular complications of Behçet disease in the Tunisian context: clinical characteristics and predictive factors

et al. 2018

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Background: Cardiac and vascular involvement in Behçet disease (BD), also referred as vasculo BD, is frequent. We aimed to describe clinical characteristics, predictive factors and management of vasculo BD in the Tunisian context. Methods: We retrospectively studied 213 records of all BD patients followed between January 2004 and May 2016 in the Internal Medicine Department and who fulfilled the ISGBD criteria. We described first clinical features of BD with cardiac and vascular involvement then predictive factors were studied in univariate then multivariate analysis. Results: Among the 213 patients, 64 (30%) were diagnosed as having vasculo BD. The mean age at diagnosis was 31.5 years. About 81.25% of them were males and 18.75% females. Vascular involvement associated or not with cardiac involvement was found in 64 patients (30%). Deep venous thromboses are most common (62.5%) compared with superficial ones (23.4%), pulmonary arterial thrombosis (14.1%) or aneurysms (9.4%). Cardiac involvement is ranging from pericarditis (1.6%) to intra cardiac thrombosis (3.1%) and myocardial infarction (1.6%). Predictive factors associated with cardiac and vascular involvement in BD are male gender (OR = 3.043, 95% CI = 1.436-6.447, p = 0.004), erythema nodosum (OR = 4.134, 95% CI = 1.541-11.091, p = 0.005) and neurologic involvement (OR = 2.46, 95% CI = 1.02-5.89, p = 0.043). Conclusion: Cardiac and vascular involvement in BD is frequent in the Tunisian context with a broad spectrum of manifestations ranging from vascular involvement to cardiac one. Male gender, patients with erythema nodosum or neurologic involvement are prone to develop cardiac or vascular features of BD needing therefore a close monitoring.

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Section: Discussionmentioning

confidence: 99%

Cardiac and vascular complications of Behçet disease in the Tunisian context: clinical characteristics and predictive factors

et al. 2018

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“…One patient had incidental diagnosis of PAA, while undergoing workup for hematuria from internal iliac aneurysm. 48 These aneurysms were multiple and in bilateral distribution in most cases. Size of these aneurysms ranged from 8 mm to 10 cm in diameter (mean: 53.31 mm).…”

Section: Acquiredmentioning

confidence: 97%

Pulmonary artery aneurysm: a review

et al. 2020

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Pulmonary artery aneurysm is a rare but important entity in the spectrum of pulmonary vascular diseases. The etiologies can be varied and patients can present with non-specific symptoms with the diagnosis being incidental. There is limited consensus regarding the diagnostic criteria and follow-up imaging for patients diagnosed with this entity. Further the management strategies can be variable depending upon underlying disease, etiology, center dependent expertise, and resources available. We review the etiologies, epidemiology, classification, clinical manifestations, and imaging features of pulmonary artery aneurysm. We also review the current management strategies and suggest an algorithmic approach to these patients.

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“…Other features such as fever are described. Apart from that, patients can present with cough, hemo- ptysis, dyspnea and chest pain related to pulmonary aneurysms [ 4 , 12 , 16 , 17 ].…”

Section: Disease Descriptionmentioning

confidence: 99%

Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome

Kéchida¹,

Daadaa²,

Jomaa³

2022

Reumatologia

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Hughes-Stovin syndrome is a rare disease characterized by thrombophlebitis associated with arterial or bronchial aneurysms. Even though it was described first in 1911, it is scarcely reported in the literature. Hughes-Stovin syndrome diagnosis is based on clinical manifestations as well as radiological findings. There are no validated criteria or specific laboratory findings to confirm the diagnosis. Computed tomography pulmonary angiography remains the gold standard for the diagnosis and follow-up of radiological findings, as they were recently described in a critical analysis of the largest cohort in the literature. The aim of this review is to draw attention to this rare but potentially fatal disease and to discuss its therapeutic options.

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Hughes-Stovin Syndrome Presenting With Hematuria

Cited by 8 publications

References 6 publications

Cardiac and vascular complications of Behçet disease in the Tunisian context: clinical characteristics and predictive factors

Cardiac and vascular complications of Behçet disease in the Tunisian context: clinical characteristics and predictive factors

Pulmonary artery aneurysm: a review

Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome

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