Hereditary Benign Intra-Epithelial Dyskeratosis (HBID)

Abstract

Hereditary Benign Intraepithelial Dyskeratosis (HBID) is a rare autosomal dominant recurring disorder of the oral and ocular mucosa first described in 1960 among Haliwa Native American Indians in North Carolina. A few cases have been reported also in other parts of the United States, South America and Europe. This report describes a case with clinical and histopathological features of HBID.