Hemophilic pseudotumor of the inferior maxilla

Haemophilic pseudotumour in two parts of the maxilla: case report

“…Other patterns of imaging features including an extensive fine trabecular bone pattern, 12 spicules perpendicular to a lesion, 13 fluid-fluid level in an osteolytic lesion 19 and periosteal strut from the cortex into a soft-tissue mass, 4,8 only new bone formation without an osteolytic portion 6 and flecks of calcification inside the lesion 1,22 have also been described in the previous reports.…”

“…In this report, we briefly summarized our case and the previous 24 studies, 1,[3][4][5][6][8][9][10][11][12][13][14][15][16][17][18][19][20][21][22][23][24][25][26] which included 32 cases, on haemophilic pseudotumours of the jaw. Table 1 shows the summary of studies conducted between 1968 and 2014, including the present case.…”

“…4,13 The treatment plan is chosen on a case-by-case basis, and most physicians have accepted that replacement therapy that provides the coagulation factor is a fundamental component of treatment and another appropriate therapy with replacement therapy is effective. 9,23 In conclusion, our case of a patient with haemophilic pseudotumour required a differential diagnosis with post-operative maxillary cysts, ameloblastoma, odontogenic cysts and fibrous dysplasia which were relatively common diseases compared with haemophilic pseudotumours.…”

Maxillary pseudotumor as initial manifestation of von Willebrand disease, type 2: report of a rare case and literature review

“…19,22,48 PTs in the maxillofacial region are uncommon, with 25 cases reported to date in the English language literature. [19][20][21][22][23][25][26][27][28][29][30][31][32][33][34][35][36][37][38][39][40] Among these examples of PTs affecting the jaws, 20 involved the mandible 19,21,[25][26][27][28][29][30][31][34][35][36][37][38][39] and 5 the maxilla. 21,32,33,34,40 Among the reported cases of PTs of the jaws, 21 were associated with FVIII deficiency and 3 with FIX deficiency.…”

“…19,20,[22][23][24] PT is uncommon in the maxillofacial region, with 25 cases reported to date in the English language literature. [19][20][21][22][23][25][26][27][28][29][30][31][32][33][34][35][36][37][38][39][40] Interestingly, all aforementioned examples of oral PTs have been associated with either hemophilia A or B. Case reports focusing on the oral manifestation of PTs in VWD remain scarce, with only one well-documented previous example involving the maxillary sinus of a patient with type 3 VWD.…”