Abbreviations: FFP, fresh frozen plasma; BSMMU, bangabandhu sheikh mujib medical university DMC, Dhaka medical college; PWH, person of world hemophilia; VAS, visual analogue scale
IntroductionHemophilia is not a common disease. It is a mostly inherited genetic disorder that impairs the body's ability to make blood clots, a process needed to stop bleeding. It is a hereditary bleeding disorder caused by a lack or absent of blood clotting factor -VIII or IX. There are two main types of haemophilia: haemophilia A, which occurs due to not enough clotting factor VIII, and haemophilia B, which occurs due to not enough clotting factor IX). Joint bleeding is common in hemophilia followed by muscle bleeding, other bleeding and brain hemorrhage. The prevalence of hemophilia is estimated to be about 1:10000 birth and that of the severe form of the disease to be about 6% per 100000 population.1 Even medical personnel are sometimes not familiar with its diagnosis and management which is pathetic. As such many health care professionals are not aware of the integral role physiotherapists play in the management of people with bleeding disorders or sometimes they refer patient to other medical professional for physiotherapy. Lack of referral system makes this problem more severe though scenario is changing day by day. Seminar, symposium, conference and workshop regarding Haemophilia can build up awareness. Physiotherapy is recognized as a mean to improve quality of life, improve healing times and decrease frequency of bleeds, and to aid in the prevention of joint destruction due to multiple bleeds.
Case historyMaster Abdullah-14years old boy is the subject under study. At his first years of birth, he used to have bruises often all over his body. They would disappear often a few days. When he was 3years old, he fell from a chair and his mouth struck at the brain of a vessel on the floor. He was taken to Bangabandhu Sheikh Mujib Medical University (BSMMU) where his condition was diagnosed as Hemophilia-A at a severe level, less than 1%. He had frequent bleeding in the right knee joint and sometime gum bleeding. At the age of 5years he had a major bleed in the urinary track and developed Hematuria. His left knee had become stiff due to prolonged bleeds and also because of a fall few years ago. The knee joint had been dislocated. He used to treat with pain killer, ice, Fresh Frozen Plasma (FFP). He started receiving factor replacement since a few years. He was admitted to school at the age of 6yrs. He had to change school since the management refused to take any care about him. At present he has no problem with teachers or schoolmates on account of hemophilia, but now he faces some problem or non-co-operation from his family members specially his father. His father thinks or believes that "It is a non-curative disease and his wife is responsible for the disease" so he is not interested to do any treatment or other co-operation even not continue education. Sometimes he also avoids his wife. From January 2017, he has been suffering rec...