Häufigkeit von Hörstörungen bei Langerhans-Zell-Histiozytose im Kindes- und Jugendalter

Abstract

We recommend periodical audiological follow up examinations for LCH patients with lesions of the temporal bone and/or the brain. BERA is indicated in cases with CNS lesions, because central auditory and speech processing disorders are possible in those patients.

Case report: Langerhans cell histiocytosis of the temporal bone in children: Challenging diagnosis of a rare disease with some pitfalls

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Langerhans cell histiocytosis (LCH) is a very rare condition with an incidence of 4-5 cases per million per year in children in Europe. 1,2 Currently, the etiology of the disease is not completely known; there is some evidence, that it is mainly caused by unchecked proliferation of Langerhans cells, which occur predominantly in children and teenagers. The course of this disease is not uniform.

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