Haemophilic pseudotumours of the mandible: Report of a case in a one-year-old child

Pseudotumor of the Mandible as First Presentation of Hemophilia in a 2-Year-Old Male: A Case Report and Review of Jaw Pseudotumors of Hemophilia

“…In only one other case besides ours [10] was Factor IX deficiency the underlying disorder, with all others reporting Factor VIII deficiency. In cases reporting severity of hemophilia, seven were reported as severe [8][9][10][11][12], two were reported as moderate [13], including our case, and three were reported as mild [9,14,15].…”

“…The left mandible was the site of most frequent occurrence (n = 8), followed by the right mandible (n = 6) (two cases had both sides of the mandible affected) [8,9], and left maxilla (n = 4). The mean age at presentation was 11.8 years (6 months-34 years).…”

“…Five cases reported an antecedent trauma to the affected region [8][9][10]16], with one of these traumatic instances associated with tooth extraction in an 11-year-old male [9].…”

“…Factor replacement alone was the treatment in three cases [8,12,16], while factor replacement plus additional treatment was given in seven cases, including ours [9][10][11]15]. The antifibrinolytic agent aminocaproic acid was used in only one case besides ours as supplemental therapy [18].…”

Haemophilic pseudotumour in two parts of the maxilla: case report

“…In this report, we briefly summarized our case and the previous 24 studies, 1,[3][4][5][6][8][9][10][11][12][13][14][15][16][17][18][19][20][21][22][23][24][25][26] which included 32 cases, on haemophilic pseudotumours of the jaw. Table 1 shows the summary of studies conducted between 1968 and 2014, including the present case.…”