Haemangiopericytoma of infratemporal fossa

Abstract

Haemangiopericytomas (HPCs) are rare vascular tumours that commonly involve the soft tissues of the trunk and lower extremities. In the head and neck, the most common sites are the nasal cavity and the paranasal sinuses, and unusually, the orbital region, the parotid gland, and the neck. We report a patient with HPC that originated in the infratemporal fossa and involved the pterygopalatine and the middle cranial fossae, apparently the first such case to be reported. Although the patient has undergone resection on three separate occasions, the tumour recurred. We then performed an extended resection using the infratemporal fossa approach type D. The patient has shown no recurrence in the past five years. Although histopathologic confirmation of this malignancy may be difficult, extensive resection remains the most effective treatment in such cases.

Hemangiopericytomas in the central nervous system

“…Patients with hemangiopericytomas may have many unusual symptoms. [37][38][39][40][41][42][43][44][45] Consistent with our observations, the CT scans reveal these tumors to be generally heterogeneous, dense, and dural-based lesions. 10,11,40,41 They are usually misdiagnosed as meningiomas before surgery.…”

Hemangiopericitoma de aurícula izquierda: Caso clínico

“…La ubicación más frecuente de estos tumores son la piel, tejido subcutáneo, músculo de las extremidades y retroperitoneo. Sin embargo, es raro encontrarlo en corazón o en mediastino 11 . El hemangiopericitoma ubicado en aurícula izquierda tiene un cuadro clínico caracterizado por disnea progresiva que luego se hace severa asociado a compromiso hemodinámico en etapas más avanzadas 2 .…”

Concurrent Cochlear Implantation with Resection of Skull Base Hemangiopericytoma Following Sudden Deafness in an Only-Hearing Ear

“…5,7-10 Skull base or temporal bone HPCs are very rare, with fewer than 15 cases reported in the literature. [11][12][13][14][15][16] Only two cases with significant intracranial extension of an ITF HPC are reported in the literature. 13,14 This is to be distinguished from primary intracranial HPC or distant metastasis.…”

“…[11][12][13][14][15][16] Only two cases with significant intracranial extension of an ITF HPC are reported in the literature. 13,14 This is to be distinguished from primary intracranial HPC or distant metastasis. 27,29,30 Interestingly, in addition to the skull base HPC, our patient had a contralateral vestibular schwannoma.…”

“…[5][6][7][8][9][10] HPC involving the skull base is very rare, with less than 15 cases reported in the literature, only two of which had significant intracranial extension. [11][12][13][14][15][16] Hearing loss attributable to skull base HPC has been described in only two cases, both low-grade tumors occurring in the middle ear space. 15,16 Cochlear implantation (CI) at the time of tumor resection is well characterized in the case of acoustic neuroma, though there are few reports of concurrent CI following ablative surgery for other tumors.…”