Giant Intrahepatic Lipoblastoma in a Child

Fanna, Martina; Rougemont, Anne‐Laure; Arni, Delphine; Toso, Christian; Anooshiravani-Dumont, Mehrak; Wildhaber, Barbara E.

doi:10.1016/j.jpeds.2019.02.040

Cited by 3 publications

(2 citation statements)

References 22 publications

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“…The accurate pre-operative diagnosis of lipoblastoma is very difficult 18 .However, USG may help to outline the mass as a highly-echogenic or sometimes with hypoechogenic patches, and CT scans can delineated a nonenhanced, fat-density and sharply marginated mass with few internal septations but cannot give any conclusive diagnosis 18,19 .Besides, image techniques may be indefinite or equivocal and do not always reliably differentiate benign from malignant tumors 20 . In our case there was also diagnostic difficulty because of inconclusive evidences of diagnostic reports.…”

Section: Discussionmentioning

confidence: 99%

A Giant Mesentric Lipoblastoma in a Two-Year Girl: A Case Report

Palit

Chakroborty

Saha

et al. 2021

J Shaheed Suhrawardy Med Coll

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Back ground: Abdominal lipoblastomas which are benign but uncommon soft tissue tumors in children rarely arise from the mesentery.However, benign, these may attain in large size and cause compression symptoms. Complete resection and close post-operative monitoring are necessary for avoidance of recurrence. Histopathology with immunohistochemistry in conjunction with the morphology is the gold standard for diagnosis. Herein such a rare a case of mesenteric lipoblastoma with huge abdominal distention is reported. Case presentation: A 2-year-old girl presented with an enormous abdominal swelling occupying almost all quadrants of the abdomen with repeated dull abdominal pain. The swelling was a non-tender and tensely cystic. USG and CT Scan could not distinguish the proper origin or location of the mass but demonstrated as a large encapsulated and lobulated fatty mass measuring about (16.4x10.0x18.6cm) involving right hypochondriac, epigastric, bilateral ilio-lumber, umbilical & hypogastric regions, pushing the bowel loops upward & laterally with mild mesenteric thickening of perilesional mesentery and separated from the liver & both kidneys and other intraabdominal organs. After exploratory laparotomy there revealed a well capsuled large (about 15x11x14cm)soft yellow mass displacing the entire intra-abdominal contents, connected by a single vascular pedicle with the mesentery and loosely enclosing the mesentery as a whole. Histology and immunohistochemistry of completely resected mass conûrmed the presence of mature adipocytes and immuno-morphology was compatible with Lipoblastoma. Conclusion: This case represents one of the largest mesenteric lipoblastomas in accordance to the patient’s age that histologically, mostly composed of mature adipocytes with few lipoblasts. J Shaheed Suhrawardy Med Coll, December 2020, Vol.12(1); 54-57

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Section: Discussionmentioning

confidence: 99%

A Giant Mesentric Lipoblastoma in a Two-Year Girl: A Case Report

Palit

Chakroborty

Saha

et al. 2021

J Shaheed Suhrawardy Med Coll

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“…Lipoblastoma may also arise in the abdomen, mesentery, retroperitoneum, pelvis, inguinoscrotal or labial region, perineum, mediastinum and head/neck region [ 2 , 11 , 13 , 14 ]. Lung, liver, heart, colon and parotid gland lipoblastomas have also been described [ 2 , 13 , 14 , 15 , 16 , 17 , 18 , 19 , 20 ]. Colonic and mesenteric cases have been associated with intussusception and volvulus [ 21 , 22 ].…”

Section: Lipoblastoma and Lipoblastomatosismentioning

confidence: 99%

Update of Pediatric Lipomatous Lesions: A Clinicopathological, Immunohistochemical and Molecular Overview

Ameloot

Cordier

Dorpe

et al. 2022

JCM

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Lipomatous neoplasms are a rare entity in the pediatric population, comprising less than 10% of soft tissue tumors in the first two decades of life. Some characteristics of pediatric adipocytic tumors are analogous to their adult counterparts, some pediatric lipomatous lesions however harbor unique features. In recent years, there have been significant advances in the understanding of the pathogenesis and hence in the classification and treatment of pediatric adipocytic tumors. This literature-based article will provide a review of the presently known clinicopathological, immunohistochemical and molecular features of pediatric lipomatous lesions.

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