Giant hydronephrosis associated with angiomyolipoma in an adult male: A case report

Abstract

Giant Hydronephrosis in the adult can reach elephantoid proportions, containing several liters of fluid. It can be associated with rare renal neoplasms. We present a 27 year old man with progressive painless abdominal distention whose imaging investigations (ultrasound and CT scan) disclosed a left GH. This was successfully removed en-bloc by simple nephrectomy via a midline laparotomy. Obstruction was at the UPJ, the mass contained 13.5L of fluid and histopathologic examination revealed Angiomyolipoma of the kidney and pelvis. This is a rare discovery in a rare pathology.

Selective angioembolization as a management strategy for angiomyolipoma causing urinary tract obstruction

“…Two prior cases of obstructing AML have been reported. 3 , 4 Each were treated surgically with excision. This report describes the first case of obstructing AML treated with angioembolization.…”

“…Only 2 cases have been reported in the literature of an AML causing urinary flow obstruction, which were treated with simple and partial nephrectomy. 3 , 4 Here we present a case of an obstructing AML successfully managed with angioembolization.…”