Functional single ventricle with extracardiac total anomalous pulmonary venous connection☆

Nakata, Tomohiro; Fujimoto, Yoshifumi; Hirose, Katsumi; Osaki, Masaki; Tosaka, Yuko; Ide, Yuya; Tachi, Maiko; Sakamoto, Kisaburo

doi:10.1016/j.ejcts.2009.02.060

Cited by 30 publications

(27 citation statements)

References 24 publications

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“…The occurrence of postoperative PVO did not reduce survival, but had a significant negative impact on Fontan completion [16]. Nakata et al [17 ]showed that 26 patients who underwent surgical repair of a functional single ventricle and extracardiac TAPVC had a survival after the repair of TAPVC of 58 and 54% at 1 and 5 years, respectively. However, TAPVC was not found to be an important contributor to mortality in our study and the mortality was very high among patients with anomalous pulmonary venous connections and PVO; 3 out of the 5 patients died.…”

Section: Discussionmentioning

confidence: 99%

Early- and Middle-Term Surgical Outcomes in Patients with Heterotaxy Syndrome

Chen

Ma²,

Cui³

et al. 2015

Cardiology

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Objectives: Heterotaxy syndrome is a recognized risk factor for surgical cardiac interventions. We evaluated the early- and middle-term results of a surgical intervention for patients with heterotaxy syndrome. Methods: A total of 42 patients with heterotaxy syndrome were enrolled (September 2008 to March 2015). Left and right atrial isomerism were identified in 26% (11 out of 42) and 74% of patients (31 out of 42), respectively. The median age of the patients at the time of surgery was 6.8 months (range: 5 days to 22.3 years). Biventricular repair was completed in 3 patients with left atrial isomerism. Seventeen out of 39 patients who were scheduled for single ventricular repair completed a modified Fontan procedure. Results: The hospital mortality rate was 4.7% (2 out of 42). Another 5 deaths occurred in the remaining survivors following hospital discharge with a follow-up duration of 45.8 ± 23.6 months (range: 13-111 months). The 1-year and 5-year survival rates were 88.1% (37/42) and 83.3% (35/42), respectively. Univariate analysis and multivariate analysis identified pulmonary venous obstruction and atrioventricular valve replacement as additional risk factors for mortality. Conclusions: Right ventricular bypass surgery remains the preferred palliative procedure for patients with heterotaxy syndrome. Based on the current results, the early- and middle-term outcomes are satisfactory.

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Section: Discussionmentioning

confidence: 99%

Early- and Middle-Term Surgical Outcomes in Patients with Heterotaxy Syndrome

Chen

Ma²,

Cui³

et al. 2015

Cardiology

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“…These risk factors include patient age at the time of repair, morphologic connection, presence of pulmonary venous obstruction, and associated cardiac defects. Recent reviews have reported the neutralization of these risk factors over the last several decades [3, 4]. The majority of this data has been produced by single center retrospective experiences [4, 5].…”

Section: Introductionmentioning

confidence: 99%

Repair of “Simple” Total Anomalous Pulmonary Venous Connection: A Review From the Pediatric Cardiac Care Consortium

Louis

Harvey

Menk

et al. 2012

The Annals of Thoracic Surgery

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Background Outcomes for repair of Total Anomalous Pulmonary Venous Connection (TAPVC) from individual institutions suggest a significant improvement in mortality over the last several decades. The purpose of this study is to review the outcomes following repair of TAPVC from a large multi-institutional registry. Methods A retrospective review of the multi-institutional database, the Pediatric Cardiac Care Consortium (PCCC) was used to identify patients with the diagnosis of TAPVC who underwent complete correction between the years of 1982 to 2007. Data reviewed included age, decade of primary operation, anatomic type, presentation, and in-hospital mortality. Results Of the 118,084 surgical procedures submitted to the PCCC, 2191 (1.9%) were primary surgical correction of TAPVC. Sixty one percent of the cohort was male with 6.8% reported as premature. Overall in-hospital surgical mortality for simple TAPVC was 13%. Mortality was 20% from 1982 to 1989, 16% from 1990 to 1999, and 8% from 2000 to 2007. Obstruction to the anomalous pulmonary venous connection occurred in 29% with a mortality of 26%. Conclusions Surgical outcomes from repair of congenital cardiac anomalies have significantly improved over the last several decades. Multi-institutional large databases are needed to confirm results published from single institutional experiences. Although improvements in surgical repair of TAPVC have occurred over the last three decades, specific subtypes still experience significant mortality.

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“…TAPVC can be associated with a univentricular heart and needs to be addressed at the time of the initial BDG or at the time of the TCPC . An unobstructed cardiac TAPVC with unrestricted mixing of blood at the atrial level is an exception because all the pulmonary venous and systemic venous return mix freely.…”

Section: Discussionmentioning

confidence: 99%

“…TAPVC can be associated with a univentricular heart and needs to be addressed at the time of the initial BDG or at the time of the TCPC. 1 An unobstructed cardiac TAPVC with unrestricted mixing of blood at the atrial level is an exception because all the pulmonary venous and systemic venous return mix freely. In our patient, this was not the case as there was restriction at the mouth of the CS and at the level of the interatrial septum, thus requiring unroofing of the CS and enlargement of the ASD.…”

Section: Discussionmentioning

confidence: 99%

An Alternative Approach for Repair of Total Anomalous Pulmonary Venous Connection to the Coronary Sinus at the Time of Extracardiac Total Cavopulmonary Connection

et al. 2013

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Functional single ventricle with extracardiac total anomalous pulmonary venous connection☆

Abstract: The mid-term results of the surgical repair of functional single ventricle with supracardiac or infracardiac TAPVC are acceptable. The surgical treatment of patients with mixed TAPVC and with severe atrioventricular valve regurgitation is not promising, but can be improved.

Cited by 30 publications

References 24 publications

Early- and Middle-Term Surgical Outcomes in Patients with Heterotaxy Syndrome

Early- and Middle-Term Surgical Outcomes in Patients with Heterotaxy Syndrome

Repair of “Simple” Total Anomalous Pulmonary Venous Connection: A Review From the Pediatric Cardiac Care Consortium

An Alternative Approach for Repair of Total Anomalous Pulmonary Venous Connection to the Coronary Sinus at the Time of Extracardiac Total Cavopulmonary Connection

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