Functional outcomes of an adult with osteogenesis imperfecta after rehabilitation post bilateral Girdlestone procedure

Abstract

This is a case of a 54-year-old woman managed as a case of osteogenesis imperfecta type 1 who sustained a left subtrochanteric fracture and eventual ankylosis of both hips after surgery and immobilisation. These injuries rendered her bedridden, maximally assisted in transitions and transfers, and unable to be positioned past 30° of backrest elevation. The patient underwent a bilateral Girdlestone procedure and had tailored progressive postoperative rehabilitation in both the inpatient and outpatient settings. The patient also continued to receive bisphosphonates during her preoperative and postoperative period, to improve bone stock and aid in relieving pain. Through the efforts of a team of physiatrists, geneticists and orthopaedic surgeons, the patient was able to achieve pain-free sitting, independent transitions and short-distance ambulation, which have allowed her to care for herself more effectively and return to her work and activities of daily living.

Girdlestone Resection Arthroplasty: A Salvage Procedure for Severe Rheumatoid Arthritis

“…Supnet, et al describe a patient with osteogenesis imperfecta who was able to achieve pain-free sitting, transition independently, and ambulate short distances [24]. Another study reported that results of Girdlestone arthroplasty appear to improve with time from surgery [25]. The patient in the current study was able to transfer and have significantly reduced hip pain after undergoing Girdlestone resection arthroplasty, which is consistent with other reports.…”