“…It is a rare disease comprising less than 2% of all dysganglionoses [32,34,55]. IND B, characterized by abnormalities in the development of the submucosal plexus, is almost as frequent as Hirschsprung's disease [34] and has been the subject of many studies [5,10,15,40,46,47,48,49,56,57,58,59,60].…”