From Cancer Mimicking Orphan Lung Disease to Orphan Thoracic Oncology

Girard, Nicolas; Cottin, Vincent; Cordier, Jean-François

doi:10.1007/978-1-4471-2401-6_35

Cited by 1 publication

(3 citation statements)

References 84 publications

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“…Although the distribution of the disease is multi organic, the most frequently affected site is the lung, presenting at the time of diagnosis with respiratory symptoms (dyspnea, cough, chest pain) and symptoms of general repercussion (fever, depression). to weight loss)Going spontaneous remissions, most present a more aggressive evolutionary course, with disease and progressive respiratory failure (3) . Over 60% of patients die within 5 years, with a median survival of 14 months.…”

Section: Discussionmentioning

confidence: 99%

“…Over 60% of patients die within 5 years, with a median survival of 14 months. (3) . Radiographic findings include multiple rounded opacities (80%) and diffuse reticulono-dullary infiltrates (Pina-Oviedo, Shroff et al 2023).…”

Section: Discussionmentioning

confidence: 99%

“…The disease was progressive, with worsening respiratory failure and death of the patient 45 days after admission. The definitive diagnosis of GL was obtained using a sample of lung parenchyma obtained by autopsy (Girard 2023).…”

Section: Case Presentationmentioning

confidence: 99%

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Lymphomatoid Granulomatous: Pulmonary Manifestations Of A Rare Entity

Hussein,

Khan,

Ullah

et al. 2024

JAZ

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Background: Lymphomatoid granulomatosis (LG) is a rare lymphoproliferative disease predominantly affecting extranodal sites, characterized by its angiocentric lymphoma nature and a notable affinity for blood vessels. Objective: To highlight the clinical and radiographic features of LG, emphasizing its primary pulmonary involvement. Methods: A case report of a 69-year-old male presenting with distinct radiographic findings via conventional chest radiography (XR) and computed tomography (CT).Results: The patient exhibited multiple bilateral cavitated nodular lesions in both XR and CT scans. Despite the diagnostic challenges and a grim clinical course, the disease was confirmed as LG post-mortem. Conclusion: Recognizing LG's distinctive pulmonary manifestations within an appropriate clinical context is pivotal for early diagnosis and intervention, albeit with a median survival of approximately 2 years

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%